{"id":105903,"date":"2020-02-02T09:32:05","date_gmt":"2020-02-02T08:32:05","guid":{"rendered":"https:\/\/sdk.mk\/?p=105903"},"modified":"2020-02-02T09:32:05","modified_gmt":"2020-02-02T08:32:05","slug":"ju-njoftojme-me-semundjet-e-rralla-fruktozemia","status":"publish","type":"post","link":"https:\/\/sdk.mk\/index.php\/histori-te-parrefyera\/ju-njoftojme-me-semundjet-e-rralla-fruktozemia\/","title":{"rendered":"JU NJOFTOJM\u00cb ME S\u00cbMUNDJET E RRALLA: FRUKTOZEMIA"},"content":{"rendered":"<div class=\"f52428582a4b906b2d2e2a7d733c7d27\" data-index=\"7\" style=\"float: none; margin:10px 0 10px 0; text-align:center;\">\n<!-- MSP Ads Asynchronous JS Tag - Generated with Revive Adserver v5.4.1 -->\r\n<ins data-revive-zoneid=\"167\" data-revive-id=\"060fdb01f6430ec164d3519234aa4967\"><\/ins>\r\n<script async src=\"\/\/panel.ads.com.mk\/www\/delivery\/asyncjs.php\"><\/script>\n<\/div>\n<p><em><strong><a href=\"https:\/\/www.youtube.com\/watch?v=5k2XyHw1SUE&amp;list=PLPGcigDEy-qj0I1um2ByEqy4a1IdVRjzf&amp;index=3&amp;t=0s\" target=\"_blank\" rel=\"noopener noreferrer\">Intoleranca e fruktoz\u00ebs trash\u00ebgimore &#8211; Fruktozemia <\/a><\/strong><\/em><br \/>\nHereditary Fructose Intolerance<\/p>\n<p>MKB E74.1<br \/>\nIntoleranca e fruktoz\u00ebs trash\u00ebgimore gjendet edhe n\u00ebn emrat: Fruktozemia, mang\u00ebsi B e fruktoz\u00ebs aldolaza, fruktoza 1, 6 mungesa e aldolaz\u00ebs bisfosfat.<\/p>\n<p>Pacient\u00ebt me k\u00ebt\u00eb s\u00ebmundje kan\u00eb munges\u00eb proteine \u200b\u200bq\u00eb degradon fruktoz\u00ebn. Fruktoza \u00ebsht\u00eb nj\u00eb sheqer frutash q\u00eb prodhohet natyrsh\u00ebm n\u00eb trup. Njer\u00ebzit gjithashtu krijojn\u00eb fruktoz\u00eb, e cila p\u00ebrdoret p\u00ebr t\u00eb \u00ebmb\u00eblsuar ushqime t\u00eb ndryshme, si dhe ushqime p\u00ebr f\u00ebmij\u00eb dhe pije.<\/p>\n<p>Shkaqet e paraqitjes s\u00eb intoleranc\u00ebs ndaj fruktoz\u00ebs dhe incidenc\u00ebs<\/p>\n<p>Kjo situate paraqitet kur trupit i mungon nj\u00eb enzim\u00eb e quajtur aldolaza B, e nevojshme p\u00ebr t\u00eb zb\u00ebrthyer fruktoz\u00ebn. N\u00ebse nj\u00eb person pa k\u00ebt\u00eb enzim\u00eb konsumon fruktoz\u00ebn dhe saharoz\u00ebn, n\u00eb trup do t\u00eb ndodhin ndryshime t\u00eb nd\u00ebrlikuara kimike pasi q\u00eb trupi nuk mund ta shnd\u00ebrroj\u00eb materialin energjetik &#8211; glukogjenin n\u00eb glukoz\u00eb. Si rezultat, sheqeri n\u00eb gjak bie dhe substanca t\u00eb rrezikshme deponohen n\u00eb m\u00ebl\u00e7i. Kjo s\u00ebmundje \u00ebsht\u00eb e trash\u00ebgueshme, q\u00eb do t\u00eb thot\u00eb se i p\u00ebrcillet an\u00ebtar\u00ebve t\u00eb familjes. N\u00ebse t\u00eb dy prind\u00ebrit mbajn\u00eb nj\u00eb gjen jo normal, secili prej f\u00ebmij\u00ebve t\u00eb tyre ka gjasa prej 25% p\u00ebr t\u00eb zhvilluar intoleranc\u00eb ndaj fruktoz\u00ebs. Kjo gjendje paraqitet tek 1 n\u00eb 20,000 njer\u00ebz n\u00eb vendet evropiane.<br \/>\nSimptomat<br \/>\nSimptomat e hershme jan\u00eb t\u00eb ngjashme me ato t\u00eb galaktozemis\u00eb nd\u00ebrsa simptomat e m\u00ebvonshme shoq\u00ebrohen me s\u00ebmundje t\u00eb m\u00ebl\u00e7is\u00eb. Disa nga simptomat q\u00eb shfaqen jan\u00eb: konvulsione, nevoja e tep\u00ebrt p\u00ebr gjum\u00eb, nervoziz\u00ebm, oreks i dob\u00ebt, probleme pas ngr\u00ebnies s\u00eb frutave dhe ushqimeve q\u00eb kan\u00eb nivel t\u00eb lart\u00eb t\u00eb fruktoz\u00ebs, t\u00eb vjella dhe dhimbje barku.<\/p>\n<p>Diagnoza<br \/>\nEkzaminimi fizik tregon m\u00ebl\u00e7i ose shpretk\u00eb t\u00eb zmadhuar \u2013 hepatosplenomegaly, l\u00ebkur\u00eb me ngjyr\u00eb t\u00eb verdh\u00eb si dhe n\u00eb pjes\u00ebn e bardh\u00eb t\u00eb syve. Testet q\u00eb konfirmojn\u00eb diagnoz\u00ebn jan\u00eb: testi i mpiksjes s\u00eb gjakut, testi i sheqerit n\u00eb gjak, testet e enzimave, testet gjenetike, testet e funksionit t\u00eb veshkave dhe m\u00ebl\u00e7is\u00eb, biopsia e m\u00ebl\u00e7is\u00eb, testet e gjakut t\u00eb acidit urik, analiz\u00eb t\u00eb urin\u00ebs. Gjat\u00eb k\u00ebtyre testeve, sheqeri n\u00eb gjak \u00ebsht\u00eb i ul\u00ebt, ve\u00e7an\u00ebrisht pas konsumit t\u00eb fruktoz\u00ebs ose saharoz\u00ebs, nd\u00ebrsa niveli I acidit urik \u00ebsht\u00eb i lart\u00eb.<\/p>\n<p>Trajtimi<br \/>\nTrajtimi m\u00eb efektiv p\u00ebr shumic\u00ebn e pacient\u00ebve \u00ebsht\u00eb heqja e fruktoz\u00ebs dhe saharoz\u00ebs nga dieta. Komplikimet trajtohen. P\u00ebr shembull, disa pacient\u00eb marrin ila\u00e7e p\u00ebr t\u00eb ulur acidin urik n\u00eb gjak, gj\u00eb q\u00eb zvog\u00eblon rrezikun e paraqitjes s\u00eb giht. Kur\u00eb p\u00ebr k\u00ebt\u00eb s\u00ebmundje do t\u00eb ishte z\u00ebvend\u00ebsimi i gjenit ose aktivitetit t\u00eb enzim\u00ebs aldolasa B drejtp\u00ebrdrejt n\u00eb m\u00ebl\u00e7i, veshk\u00eb dhe organet e brendshme. Nuk ekziston nj\u00eb kur\u00eb e till\u00eb sot, por \u00ebsht\u00eb duke u hulumtuar p\u00ebr t\u00eb gjetur di\u00e7ka q\u00eb mund t\u00eb ndihmoj\u00eb n\u00eb k\u00ebt\u00eb s\u00ebmundje.<br \/>\nParashikimi<br \/>\nIntoleranca e fruktoz\u00ebs e trash\u00ebguar mund t\u00eb paraqitet n\u00eb form\u00eb t\u00eb but\u00eb dhe t\u00eb r\u00ebnd\u00eb. Shumica e f\u00ebmij\u00ebve ndihmohen nga nj\u00eb diet\u00eb q\u00eb shmang fruktoz\u00ebn dhe saharoz\u00ebn n\u00eb diet\u00ebn e tyre tek f\u00ebmij\u00ebt q\u00eb ballafaqohen me form\u00ebn e bute. Tek ata q\u00eb kan\u00eb nj\u00eb form\u00eb t\u00eb r\u00ebnd\u00eb mund t\u00eb zhvillojn\u00eb s\u00ebmundje sezonale t\u00eb m\u00ebl\u00e7is\u00eb. Sa e mire do t\u00eb jet\u00eb cil\u00ebsia e jet\u00ebs varet nga ajo sa her\u00ebt b\u00ebhet diagnoza, sa m\u00eb her\u00ebt \u00ebsht\u00eb kufizuar dieta e fruktoz\u00ebs dhe saharoz\u00ebs aq m\u00eb mir\u00eb funksionon enzima n\u00eb trup.<br \/>\nKomplikime<br \/>\nKomplikimet q\u00eb mund t\u00eb ndodhin p\u00ebrfshijn\u00eb: gjakderdhje, vdekje, p\u00ebrdhes, mosfunksionim t\u00eb m\u00ebl\u00e7is\u00eb, sheqer t\u00eb ul\u00ebt n\u00eb gjak, sulme.<\/p>\n\n<div style=\"font-size: 0px; height: 0px; line-height: 0px; margin: 0; padding: 0; clear: both;\"><\/div>","protected":false},"excerpt":{"rendered":"<p>Intoleranca e fruktoz\u00ebs trash\u00ebgimore &#8211; Fruktozemia Hereditary Fructose Intolerance MKB E74.1 Intoleranca e fruktoz\u00ebs trash\u00ebgimore gjendet edhe n\u00ebn emrat: Fruktozemia, [&hellip;]<\/p>\n","protected":false},"author":24,"featured_media":105896,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_mo_disable_npp":"","inline_featured_image":false},"categories":[3085],"tags":[],"imageURL":"https:\/\/sdk.mk\/wp-content\/uploads\/2020\/01\/02-Hereditary-Fructose-Intolerance-650x366.png","thumbURL":"https:\/\/sdk.mk\/wp-content\/uploads\/2020\/01\/02-Hereditary-Fructose-Intolerance-250x141.png","categoryNames":["Histori t\u00eb parr\u00ebfyera"],"feature_caption":"","subtitle":"","views":"1465","source":"\u0421\u043a\u043e\u043f\u0458\u0435, (\u0421\u0410\u041a\u0410\u041c\u0414\u0410\u041a\u0410\u0416\u0410\u041c.\u041c\u041a)","yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v15.0 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>JU NJOFTOJM\u00cb ME S\u00cbMUNDJET E RRALLA: FRUKTOZEMIA - \u0421\u0430\u043a\u0430\u043c \u0414\u0430 \u041a\u0430\u0436\u0430\u043c<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/sdk.mk\/index.php\/histori-te-parrefyera\/ju-njoftojme-me-semundjet-e-rralla-fruktozemia\/\" \/>\n<meta property=\"og:locale\" content=\"mk_MK\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"JU NJOFTOJM\u00cb ME S\u00cbMUNDJET E RRALLA: FRUKTOZEMIA - \u0421\u0430\u043a\u0430\u043c \u0414\u0430 \u041a\u0430\u0436\u0430\u043c\" \/>\n<meta property=\"og:description\" content=\"Intoleranca e fruktoz\u00ebs trash\u00ebgimore &#8211; 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