{"id":106478,"date":"2020-02-08T08:34:47","date_gmt":"2020-02-08T07:34:47","guid":{"rendered":"https:\/\/sdk.mk\/?p=106478"},"modified":"2020-02-08T08:34:47","modified_gmt":"2020-02-08T07:34:47","slug":"ju-njoftojme-me-semundjet-e-rralla-sindroma-brugada","status":"publish","type":"post","link":"https:\/\/sdk.mk\/index.php\/histori-te-parrefyera\/ju-njoftojme-me-semundjet-e-rralla-sindroma-brugada\/","title":{"rendered":"JU NJOFTOJM\u00cb ME S\u00cbMUNDJET E RRALLA: SINDROMA BRUGADA"},"content":{"rendered":"<div class=\"f52428582a4b906b2d2e2a7d733c7d27\" data-index=\"7\" style=\"float: none; margin:10px 0 10px 0; text-align:center;\">\n<!-- MSP Ads Asynchronous JS Tag - Generated with Revive Adserver v5.4.1 -->\r\n<ins data-revive-zoneid=\"167\" data-revive-id=\"060fdb01f6430ec164d3519234aa4967\"><\/ins>\r\n<script async src=\"\/\/panel.ads.com.mk\/www\/delivery\/asyncjs.php\"><\/script>\n<\/div>\n<p><a href=\"https:\/\/www.youtube.com\/watch?v=zrtZSHnvz3M&amp;list=PLPGcigDEy-qj0I1um2ByEqy4a1IdVRjzf&amp;index=9&amp;t=0s\" target=\"_blank\" rel=\"noopener noreferrer\"><em><strong>Sindroma Brugada<\/strong><\/em><\/a><br \/>\nBrugada syndrome<br \/>\nKNS I 47.2<\/p>\n<p>Sindroma Brugada \u00ebsht\u00eb \u00e7rregullim gjenetik i cili karakterizohet me abnormalitete n\u00eb<br \/>\nregjistrimet e EKG dhe rrezik p\u00ebr vdekje t\u00eb papritur. Emrin e mban nga v\u00ebllez\u00ebrit mjek\u00eb Pedro<br \/>\ndhe Josep Brugada.<br \/>\nSindroma Brugada \u00ebsht\u00eb \u00e7rregullim i trash\u00ebguar i cili ve\u00e7ohet me disfunkcione<br \/>\nelektrofiziologjike t\u00eb zemr\u00ebs. Zakonisht pacient\u00ebt nuk kan\u00eb s\u00ebmundje t\u00eb struktur\u00ebs s\u00eb zemr\u00ebs,<br \/>\ndo t\u00eb thot\u00eb miokardi \u00ebsht\u00eb normal n\u00eb aspektin e pompimit dhe qarkullimit t\u00eb gjakut.<br \/>\nSindroma Brugada \u00ebsht\u00eb nj\u00eb patologji trash\u00ebguesse e shkaktuar nga mutacioni autosomal<br \/>\ndominant t\u00eb nj\u00eb gjeni specifik n\u00eb kromozom\u00ebn e tret\u00eb. Ajo q\u00eb e b\u00ebn k\u00ebt\u00eb s\u00ebmundje t\u00eb<br \/>\nrrezikshme p\u00ebr sh\u00ebndetin dhe jet\u00ebn vjen nga fakti q\u00eb shkakton zhvillimin e aritmive t\u00eb r\u00ebnda<br \/>\ndhe vdekje t\u00eb papritur nga sulmi kardiak. Paraqitet te meshkuj t\u00eb rinj t\u00eb mosh\u00ebs 25-45 vje\u00e7.<br \/>\nSimptomat e k\u00ebsaj sindrome jan\u00eb m\u00eb t\u00eb shpeshta n\u00eb regjionin e Kaukazit, Lindjen e larg\u00ebt, Azin\u00eb<br \/>\nJuglindore, si dhe n\u00eb Japoni, Tajland\u00eb dhe ishujt e Filipineve.<br \/>\nBrugada shfaqet p\u00ebr shkak t\u00eb \u00e7rregullimit t\u00eb struktur\u00ebs t\u00eb nj\u00eb nga 6 gjenet e njohura. E gjith\u00eb<br \/>\nkjo e \u00e7rregullon funksionimin e molekulave dhe kanaleve t\u00eb natriumit dhe kalciumit n\u00eb<br \/>\nsip\u00ebrfaqen e qelizave t\u00eb zemr\u00ebs. Ekzistojn\u00eb ndryshime patologjike n\u00eb pro\u00e7eset t\u00eb lidhura me<br \/>\npun\u00ebn e sistemit p\u00ebr\u00e7ues t\u00eb zemr\u00ebs. N\u00eb t\u00eb njejt\u00ebn koh\u00eb, mutacioni i shkaktuar mund t\u00eb<br \/>\nshkaktoj\u00eb edhe \u00e7rregullime t\u00eb tjera n\u00eb trup, pasi q\u00eb kjo sekuenc\u00eb e AND-s\u00eb \u00ebsht\u00eb p\u00ebrgjegj\u00ebse<br \/>\np\u00ebr sintez\u00ebn e enzimave t\u00eb ndryshme.<br \/>\nMe zhvillimin e sindrom\u00ebs, ndryshon transporti i jonit t\u00eb natriumit, p\u00ebr\u00e7ueshm\u00ebria e<br \/>\nmembran\u00ebs dhe kontraksioni i fijeve muskulore. \u00cbsht\u00eb i \u00e7rregulluar p\u00ebr\u00e7imi i informatave n\u00eb<br \/>\nform\u00eb t\u00eb impulseve elektrike p\u00ebrmes kardiomiociteve, t\u00eb cil\u00ebt jan\u00eb p\u00ebrgjegj\u00ebs p\u00ebr kanalet e<br \/>\nnatriumit. Shfaqet dob\u00ebsim i zemr\u00ebs, \u00e7rregullim n\u00eb kontraksionin dhe relaksimin e koordinuar<br \/>\nt\u00eb qelizave t\u00eb miokardit. Simptomat e sindrom\u00ebs shpesh shfaqen gjat\u00eb nat\u00ebs gjersa personi<br \/>\n\u00ebsht\u00eb n\u00eb gjum\u00eb.<\/p>\n<p>Simptomat dhe shenjat e zakonshme:<br \/>\n&#8211; aritmi<br \/>\n&#8211; asteni<br \/>\n&#8211; rrahje t\u00eb zemr\u00ebs<br \/>\n&#8211; dispne<br \/>\n&#8211; dhimbje gjoksi<\/p>\n<p>&#8211; gul\u00e7im<br \/>\n&#8211; fibrilacion ventrikular<br \/>\n&#8211; ankth<br \/>\n&#8211; pagjum\u00ebsi<br \/>\n&#8211; shqet\u00ebsim<br \/>\n&#8211; zbehje<br \/>\n&#8211; sinkop\u00eb t\u00eb hershme<br \/>\n&#8211; sinkop\u00eb<br \/>\n&#8211; tahikardi<br \/>\n&#8211; tahipne<br \/>\n&#8211; marramendje<br \/>\nZakonisht simptomat shfaqen n\u00eb dekad\u00ebn e tret\u00eb gjer n\u00eb dekad\u00ebn e kat\u00ebr t\u00eb jet\u00ebs. N\u00eb disa<br \/>\nraste, sindroma Brugada nuk shkakton asnj\u00eb simptom\u00eb edhe pse n\u00eb regjistrimin e<br \/>\nelketrokardiogram\u00ebs do t\u00eb v\u00ebrrehen ndryshime karakteristike. Por, prap\u00eb se prap\u00eb te shumica e<br \/>\npacient\u00ebve kjo gj\u00ebndje shpie gjer te humbja e vet\u00ebdijes si pasoj\u00eb e kontraksionit t\u00eb shpejt\u00eb dhe<br \/>\njoefikas t\u00eb barkushave t\u00eb zemr\u00ebs. Zakonisht k\u00ebto manifestime nuk jan\u00eb t\u00eb lidhura me ngarkes\u00eb<br \/>\ndhe mund t\u00eb shfaqen edhe n\u00eb koh\u00eb pushimi edhe gjat\u00eb gjumit. Episodet e sinkop\u00ebs, gjithashtu<br \/>\nmund t\u00eb shkaktohen nga ethet, ushqimi i bollsh\u00ebm dhe trajtimi me disa medikamente (duke<br \/>\np\u00ebrfshir\u00eb antiaritmik\u00eb dhe antidepresiv\u00eb). Njer\u00ebzit me sindrom\u00ebn Brugada gjithashtu mund t\u00eb<br \/>\nparaqesin palpitacione me plog\u00ebshti dhe enurez\u00eb gjat\u00eb nat\u00ebs .<br \/>\nGjat\u00eb formave dhe rasteve t\u00eb r\u00ebnda, fibrilacioni ventrikular mund t\u00eb sjell gjer te sulmi kardiak<br \/>\ndhe t\u00eb shkaktoj\u00eb vdekje t\u00eb papritur te pacienti.<br \/>\nDiagnoza bazohet n\u00eb ekzaminimin klinik dhe elektrokardiogram\u00ebn. N\u00eb disa raste, manifestimet<br \/>\nn\u00eb EKG nuk jan\u00eb specifike. N\u00eb ato raste dh\u00ebnja e antiaritmik\u00ebve \u00ebsht\u00eb e nevojshme p\u00ebr<br \/>\nv\u00ebrtetimin apo eliminimin e diagnoz\u00ebs. Gjithashtu, \u00ebsht\u00eb e mundshme edhe analiza gjenetike.<br \/>\nDiagnostikimi prenatal b\u00ebhet shum\u00eb rrall\u00eb.<br \/>\nShum\u00eb v\u00ebshtir\u00eb \u00ebsht\u00eb t\u00eb vler\u00ebsohet p\u00ebrfshirja e s\u00ebmundjes. Prevalenca n\u00eb vendet e Lindjes<br \/>\nparaqet 1\/700 -1\/800. Kurse prevalenca n\u00eb Europ\u00eb dhe n\u00eb SHBA \u00ebsht\u00eb m\u00eb e vog\u00ebl: 1\/3,300 gjer<br \/>\n1\/10,000. \u00cbsht\u00eb paraqitur form\u00eb autosomale dominante t\u00eb trash\u00ebgimit.<br \/>\nNj\u00eb defibrilator kardioverter implantues (ICD) q\u00eb vendoset n\u00ebn l\u00ebkur\u00eb \u00ebsht\u00eb opsioni terapeutik i<br \/>\nvet\u00ebm efikas te pacient\u00ebt t\u00eb cil\u00ebt kan\u00eb episode t\u00eb sinkopave dhe k\u00ebrkojn\u00eb reanimin t\u00eb shpejt\u00eb.<br \/>\nK\u00ebto pajisje e analizojn\u00eb ritmin e zemr\u00ebs n\u00eb vazhdim dhe intervenojn\u00eb n\u00eb rast t\u00eb shfaqjes s\u00eb<br \/>\naritmive ventrikulare, t\u00eb rrezikshme p\u00ebr jet\u00ebn. Po s\u00ebrish nuk \u00ebsht\u00eb e qart\u00eb cili \u00ebsht\u00eb trajtimi m\u00eb i<br \/>\nmire p\u00ebr pacient\u00ebt me ndryshime t\u00eb EKG-s\u00eb dhe histori familjare p\u00ebr rrezik nga vdekja e<br \/>\npapritur. N\u00eb p\u00ebrgjith\u00ebsi, pacient\u00ebt me sindrom\u00ebn Brugada k\u00ebshillohen q\u00eb t\u00eb evitojn\u00eb barna t\u00eb<br \/>\ncaktuara dhe situata q\u00eb mund t\u00eb shkaktojn\u00eb aritmi t\u00eb rrezikshme p\u00ebr jet\u00ebn e tyre.<\/p>\n\n<div style=\"font-size: 0px; height: 0px; line-height: 0px; margin: 0; padding: 0; clear: both;\"><\/div>","protected":false},"excerpt":{"rendered":"<p>Sindroma Brugada Brugada syndrome KNS I 47.2 Sindroma Brugada \u00ebsht\u00eb \u00e7rregullim gjenetik i cili karakterizohet me abnormalitete n\u00eb regjistrimet e [&hellip;]<\/p>\n","protected":false},"author":24,"featured_media":106475,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_mo_disable_npp":"","inline_featured_image":false},"categories":[3085],"tags":[],"imageURL":"https:\/\/sdk.mk\/wp-content\/uploads\/2020\/02\/08-Brugada-syndrome-650x366.png","thumbURL":"https:\/\/sdk.mk\/wp-content\/uploads\/2020\/02\/08-Brugada-syndrome-250x141.png","categoryNames":["Histori t\u00eb parr\u00ebfyera"],"feature_caption":"","subtitle":"","views":"1855","source":"\u0421\u043a\u043e\u043f\u0458\u0435, (\u0421\u0410\u041a\u0410\u041c\u0414\u0410\u041a\u0410\u0416\u0410\u041c.\u041c\u041a)","yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v15.0 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>JU NJOFTOJM\u00cb ME S\u00cbMUNDJET E RRALLA: SINDROMA BRUGADA - \u0421\u0430\u043a\u0430\u043c \u0414\u0430 \u041a\u0430\u0436\u0430\u043c<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/sdk.mk\/index.php\/histori-te-parrefyera\/ju-njoftojme-me-semundjet-e-rralla-sindroma-brugada\/\" \/>\n<meta property=\"og:locale\" content=\"mk_MK\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"JU NJOFTOJM\u00cb ME S\u00cbMUNDJET E RRALLA: SINDROMA BRUGADA - \u0421\u0430\u043a\u0430\u043c \u0414\u0430 \u041a\u0430\u0436\u0430\u043c\" \/>\n<meta property=\"og:description\" content=\"Sindroma Brugada Brugada syndrome KNS I 47.2 Sindroma Brugada \u00ebsht\u00eb \u00e7rregullim gjenetik i cili karakterizohet me abnormalitete n\u00eb regjistrimet e [&hellip;]\" \/>\n<meta property=\"og:url\" content=\"https:\/\/sdk.mk\/index.php\/histori-te-parrefyera\/ju-njoftojme-me-semundjet-e-rralla-sindroma-brugada\/\" \/>\n<meta property=\"og:site_name\" content=\"\u0421\u0430\u043a\u0430\u043c \u0414\u0430 \u041a\u0430\u0436\u0430\u043c\" \/>\n<meta property=\"article:published_time\" content=\"2020-02-08T07:34:47+00:00\" \/>\n<meta property=\"og:image\" content=\"https:\/\/sdk.mk\/wp-content\/uploads\/2020\/02\/08-Brugada-syndrome.png\" \/>\n\t<meta property=\"og:image:width\" content=\"1920\" \/>\n\t<meta property=\"og:image:height\" content=\"1080\" \/>\n<meta property=\"fb:app_id\" content=\"2407985809428537\" \/>\n<meta name=\"twitter:card\" content=\"summary\" \/>\n<script type=\"application\/ld+json\" class=\"yoast-schema-graph\">{\"@context\":\"https:\/\/schema.org\",\"@graph\":[{\"@type\":\"WebSite\",\"@id\":\"https:\/\/sdk.mk\/#website\",\"url\":\"https:\/\/sdk.mk\/\",\"name\":\"\\u0421\\u0430\\u043a\\u0430\\u043c \\u0414\\u0430 \\u041a\\u0430\\u0436\\u0430\\u043c\",\"description\":\"\\u0417\\u0430 \\u0441\\u043b\\u043e\\u0431\\u043e\\u0434\\u043e\\u0443\\u043c\\u043d\\u0438\",\"potentialAction\":[{\"@type\":\"SearchAction\",\"target\":\"https:\/\/sdk.mk\/?s={search_term_string}\",\"query-input\":\"required name=search_term_string\"}],\"inLanguage\":\"mk-MK\"},{\"@type\":\"ImageObject\",\"@id\":\"https:\/\/sdk.mk\/index.php\/histori-te-parrefyera\/ju-njoftojme-me-semundjet-e-rralla-sindroma-brugada\/#primaryimage\",\"inLanguage\":\"mk-MK\",\"url\":\"https:\/\/sdk.mk\/wp-content\/uploads\/2020\/02\/08-Brugada-syndrome.png\",\"width\":1920,\"height\":1080},{\"@type\":\"WebPage\",\"@id\":\"https:\/\/sdk.mk\/index.php\/histori-te-parrefyera\/ju-njoftojme-me-semundjet-e-rralla-sindroma-brugada\/#webpage\",\"url\":\"https:\/\/sdk.mk\/index.php\/histori-te-parrefyera\/ju-njoftojme-me-semundjet-e-rralla-sindroma-brugada\/\",\"name\":\"JU NJOFTOJM\\u00cb ME S\\u00cbMUNDJET E RRALLA: SINDROMA BRUGADA - \\u0421\\u0430\\u043a\\u0430\\u043c \\u0414\\u0430 \\u041a\\u0430\\u0436\\u0430\\u043c\",\"isPartOf\":{\"@id\":\"https:\/\/sdk.mk\/#website\"},\"primaryImageOfPage\":{\"@id\":\"https:\/\/sdk.mk\/index.php\/histori-te-parrefyera\/ju-njoftojme-me-semundjet-e-rralla-sindroma-brugada\/#primaryimage\"},\"datePublished\":\"2020-02-08T07:34:47+00:00\",\"dateModified\":\"2020-02-08T07:34:47+00:00\",\"author\":{\"@id\":\"https:\/\/sdk.mk\/#\/schema\/person\/864d4cb4c82a45f771023b00a4aa5176\"},\"inLanguage\":\"mk-MK\",\"potentialAction\":[{\"@type\":\"ReadAction\",\"target\":[\"https:\/\/sdk.mk\/index.php\/histori-te-parrefyera\/ju-njoftojme-me-semundjet-e-rralla-sindroma-brugada\/\"]}]},{\"@type\":\"Person\",\"@id\":\"https:\/\/sdk.mk\/#\/schema\/person\/864d4cb4c82a45f771023b00a4aa5176\",\"name\":\"Biljana Nestoroska\"}]}<\/script>\n<!-- \/ Yoast SEO Premium plugin. -->","_links":{"self":[{"href":"https:\/\/sdk.mk\/index.php\/wp-json\/wp\/v2\/posts\/106478"}],"collection":[{"href":"https:\/\/sdk.mk\/index.php\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/sdk.mk\/index.php\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/sdk.mk\/index.php\/wp-json\/wp\/v2\/users\/24"}],"replies":[{"embeddable":true,"href":"https:\/\/sdk.mk\/index.php\/wp-json\/wp\/v2\/comments?post=106478"}],"version-history":[{"count":0,"href":"https:\/\/sdk.mk\/index.php\/wp-json\/wp\/v2\/posts\/106478\/revisions"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/sdk.mk\/index.php\/wp-json\/wp\/v2\/media\/106475"}],"wp:attachment":[{"href":"https:\/\/sdk.mk\/index.php\/wp-json\/wp\/v2\/media?parent=106478"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/sdk.mk\/index.php\/wp-json\/wp\/v2\/categories?post=106478"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/sdk.mk\/index.php\/wp-json\/wp\/v2\/tags?post=106478"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}