{"id":106767,"date":"2020-02-12T12:07:54","date_gmt":"2020-02-12T11:07:54","guid":{"rendered":"https:\/\/sdk.mk\/?p=106767"},"modified":"2020-02-16T08:44:43","modified_gmt":"2020-02-16T07:44:43","slug":"ju-njoftojme-me-semundjet-e-rralla-sindroma-lennox-gastaut","status":"publish","type":"post","link":"https:\/\/sdk.mk\/index.php\/uncategorized-sq\/ju-njoftojme-me-semundjet-e-rralla-sindroma-lennox-gastaut\/","title":{"rendered":"JU NJOFTOJM\u00cb ME S\u00cbMUNDJET E RRALLA: SINDROMA LENNOX \u2013 GASTAUT"},"content":{"rendered":"<div class=\"f52428582a4b906b2d2e2a7d733c7d27\" data-index=\"7\" style=\"float: none; margin:10px 0 10px 0; text-align:center;\">\n<!-- MSP Ads Asynchronous JS Tag - Generated with Revive Adserver v5.4.1 -->\r\n<ins data-revive-zoneid=\"167\" data-revive-id=\"060fdb01f6430ec164d3519234aa4967\"><\/ins>\r\n<script async src=\"\/\/panel.ads.com.mk\/www\/delivery\/asyncjs.php\"><\/script>\n<\/div>\n<p><a href=\"https:\/\/www.youtube.com\/watch?v=KJruXnzGsJc&amp;list=PLPGcigDEy-qj0I1um2ByEqy4a1IdVRjzf&amp;index=13&amp;t=0s\" target=\"_blank\" rel=\"noopener noreferrer\"><em><strong>Sindroma Lennox \u2013 Gastaut<\/strong><\/em><\/a><br \/>\nLennox-Gastaut syndrome<br \/>\nKNS G 40.4<br \/>\nEncefalopatia infantile epileptike \u2013 sindroma Lennox \u2013 Gastaut \u00ebsht\u00eb nj\u00eb form\u00eb shum\u00eb e r\u00ebnd\u00eb e sindromit epileptik infantil q\u00eb p\u00ebrb\u00ebn 1-4% t\u00eb epilepsis\u00eb infantile dhe zakonisht shfaqet mes vitit t\u00eb dyt\u00eb dhe t\u00eb gjasht\u00eb t\u00eb jet\u00ebs. Simptomat e sindrom\u00ebs jan\u00eb lloj\u00eb t\u00eb ndryshme t\u00eb sulmeve, rezistenca ndaj barnave dhe ndaj trajtimeve, retardimi mendor ose regresioni dhe EEG-ja abnormale.<br \/>\nDisa nga shkaqet e njohura p\u00ebrfshijn\u00eb l\u00ebndime t\u00eb trurit gjat\u00eb shtatzanis\u00eb (duke e p\u00ebrfshir\u00eb k\u00ebtu edhe asfiskin\u00eb, pesha e vog\u00ebl gjat\u00eb lindjes ose lindja e parakoshme), infeksione t\u00eb r\u00ebnda t\u00eb trurit (p\u00ebrfshin encefalitin, meningitin dhe rubeol\u00ebn), malformime gjat\u00eb zhvillimit t\u00eb trurit ose histori t\u00eb konvulsioneve infantile. N\u00eb 30-35% e rasteve nuk mund t\u00eb v\u00ebrtetohet shkaku i sakt\u00eb p\u00ebr paraqitjen e s\u00ebmundjes.<\/p>\n<p>Numri m\u00eb i madh i f\u00ebmij\u00ebve zhvillohen normal kur p\u00ebr her\u00eb t\u00eb par\u00eb do t\u00eb diagnostikohen me sindrom\u00ebn Lennox \u2013 Gastaut, por pastaj ata fillojn\u00eb ti humbin aft\u00ebsit\u00eb e tyre q\u00eb i kan\u00eb arritur gjer n\u00eb at\u00eb \u00e7ast, ndonj\u00ebher\u00eb kjo ndodh n\u00eb m\u00ebnyr\u00eb dramatike, me kriza konvulsive t\u00eb pakontrolluara. F\u00ebmij\u00ebt e vegj\u00ebl mund t\u00eb shfaqin \u00e7rregullime n\u00eb sjelljen e tyre, \u00e7rregullime t\u00eb personalitetit, disponim labil dhe zhvillim psikomotorik t\u00eb vonuar. \u00c7rregullimi n\u00eb sjellje mund t\u00eb p\u00ebrfshij\u00eb veti t\u00eb k\u00ebqija sociale dhe sjellje e cila k\u00ebrkon p\u00ebrkujdesje. T\u00eb njejtat mund t\u00eb jen\u00eb t\u00eb shkaktuara edhe nga efekti i medikamenteve, v\u00ebshtir\u00ebsi gjat\u00eb interpretimit t\u00eb informatave ose \u00e7rregullime elektrike n\u00eb tru. Disa f\u00ebmij\u00eb kan\u00eb prirje t\u00eb zhvillojn\u00eb status epileptik. Kjo situat\u00eb k\u00ebrkon nd\u00ebrhyrje t\u00eb shpejt\u00eb mjek\u00ebsore.<br \/>\nAshtu si\u00e7 rriten f\u00ebmij\u00ebt me k\u00ebt\u00eb sindrom\u00eb, ndryshon edhe karakteri i sulmeve. N\u00eb t\u00eb shumt\u00ebn e rasteve, m\u00eb von\u00eb paraqiten kriza konvulsive parciale t\u00eb thjeshta dhe t\u00eb p\u00ebrb\u00ebra dhe sulme sekondare t\u00eb gjeneralizuara. Krizat konvulsive q\u00eb nuk vihen n\u00ebn kontroll mund t\u00eb jen\u00eb problemi m\u00eb i vog\u00ebl, pasi q\u00eb f\u00ebmij\u00ebt rriten, por \u00e7rregullimi n\u00eb funksionimin intelektual dhe problemet me sjelljen mbeten prezent t\u00ebr\u00eb koh\u00ebn. F\u00ebmij\u00ebt m\u00eb t\u00eb m\u00ebdhenj mund t\u00eb ken\u00eb episode t\u00eb psikoz\u00ebs, gjat\u00eb s\u00eb cil\u00ebs shprehet nj\u00eb agresivitet, probleme me karakterin dhe ngacmueshm\u00ebri. Problemet kognitive p\u00ebrfshijn\u00eb reaksion t\u00eb ngadalsuar dhe p\u00ebrpunim i ngadalsh\u00ebm i informatave. Karakteristikat kryesore t\u00eb ngecjes mentale manifestohen si apati, probleme me kujtes\u00ebn, nngadalsim i aft\u00ebsive motorike.<br \/>\nF\u00ebmij\u00ebt e shkollave mund t\u00eb vendosen n\u00eb klasa t\u00eb ve\u00e7anta ose m\u00ebsim t\u00eb ve\u00e7ant\u00eb. Prind\u00ebrit dhe tutor\u00ebt ndoshta do duhet t\u00eb mendojn\u00eb p\u00ebr opsionet n\u00eb t\u00eb ardhmen p\u00ebr f\u00ebmij\u00ebn e tyre, duke e p\u00ebrfshir\u00eb kujdestarin\u00eb, pushim t\u00eb p\u00ebrkohsh\u00ebm ose ndonj\u00eb lloj institucioni ose programi special.<\/p>\n<p>Prognoza ndryshon shum\u00eb nga personi n\u00eb person. Sh\u00ebrim i plot\u00eb, me zhdukje t\u00eb sulmeve dhe zhvillim dhe ritje normale, \u00ebsht\u00eb i pabesuesh\u00ebm p\u00ebr nj\u00eb f\u00ebmij\u00eb me k\u00ebt\u00eb sindrom\u00eb. Edhe pse nuk ka sh\u00ebrim, ekzistojn\u00eb num\u00ebr i madh i mund\u00ebsive p\u00ebr trajtim, duke e p\u00ebrmendur diet\u00ebn ketogjenike, terapi me stimulimin e nervit vagus, operacion dhe medikamente antiepileptike (medikamente q\u00eb p\u00ebrdoren p\u00ebr ti penguar sulmet konvulsive).<br \/>\nMenaxhimi dhe trajtimi:<br \/>\nTrajtimi i k\u00ebsaj gjendjeje zakonisht sjell probleme, pasi q\u00eb kjo sindrom\u00eb \u00ebsht\u00eb rezistente ndaj terapis\u00eb konvencionale. Disa nga antiepileptik\u00ebt e ri (felbamat, lamotrigin, topiramat dhe levetiracetam) u treguan si efikas n\u00eb kontrollin e sulmeve konvulsive te kjo sindrom\u00eb. Bari rufinamid mori lejen e p\u00ebrdorimit n\u00eb Europ\u00eb n\u00eb janar t\u00eb vitit 2007.<br \/>\nPrognoza:<br \/>\nShkalla e vdekshm\u00ebris\u00eb \u00ebsht\u00eb rreth 5%, por rrall\u00eb \u00ebsht\u00eb e lidhur drejp\u00ebrdrejt me vet\u00eb epilepsin\u00eb. Zakonisht rastet q\u00eb mbarojn\u00eb me vdekje jan\u00eb pasoj\u00eb e aksidenteve ose episodeve t\u00eb statusit epileptik.<\/p>\n\n<div style=\"font-size: 0px; height: 0px; line-height: 0px; margin: 0; padding: 0; clear: both;\"><\/div>","protected":false},"excerpt":{"rendered":"<p>Sindroma Lennox \u2013 Gastaut Lennox-Gastaut syndrome KNS G 40.4 Encefalopatia infantile epileptike \u2013 sindroma Lennox \u2013 Gastaut \u00ebsht\u00eb nj\u00eb form\u00eb [&hellip;]<\/p>\n","protected":false},"author":24,"featured_media":106765,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_mo_disable_npp":"","inline_featured_image":false},"categories":[1794],"tags":[],"imageURL":"https:\/\/sdk.mk\/wp-content\/uploads\/2020\/02\/12-Lennox-Gastaut-syndrome-1-650x366.png","thumbURL":"https:\/\/sdk.mk\/wp-content\/uploads\/2020\/02\/12-Lennox-Gastaut-syndrome-1-250x141.png","categoryNames":["Uncategorized"],"feature_caption":"","subtitle":"","views":"1632","source":"\u0421\u043a\u043e\u043f\u0458\u0435, (\u0421\u0410\u041a\u0410\u041c\u0414\u0410\u041a\u0410\u0416\u0410\u041c.\u041c\u041a)","yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v15.0 - 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