{"id":107431,"date":"2020-02-22T08:38:38","date_gmt":"2020-02-22T07:38:38","guid":{"rendered":"https:\/\/sdk.mk\/?p=107431"},"modified":"2020-02-22T08:38:38","modified_gmt":"2020-02-22T07:38:38","slug":"ju-njoftojme-me-semundjet-e-rralla-policitemia-rubra-vera","status":"publish","type":"post","link":"https:\/\/sdk.mk\/index.php\/uncategorized-sq\/ju-njoftojme-me-semundjet-e-rralla-policitemia-rubra-vera\/","title":{"rendered":"JU NJOFTOJM\u00cb ME S\u00cbMUNDJET E RRALLA: POLICITEMIA RUBRA VERA"},"content":{"rendered":"<div class=\"f52428582a4b906b2d2e2a7d733c7d27\" data-index=\"7\" style=\"float: none; margin:10px 0 10px 0; text-align:center;\">\n<!-- MSP Ads Asynchronous JS Tag - Generated with Revive Adserver v5.4.1 -->\r\n<ins data-revive-zoneid=\"167\" data-revive-id=\"060fdb01f6430ec164d3519234aa4967\"><\/ins>\r\n<script async src=\"\/\/panel.ads.com.mk\/www\/delivery\/asyncjs.php\"><\/script>\n<\/div>\n<p><a href=\"https:\/\/www.youtube.com\/watch?v=GKsBSWqmkhA&amp;list=PLPGcigDEy-qj0I1um2ByEqy4a1IdVRjzf&amp;index=23&amp;t=0s\" target=\"_blank\" rel=\"noopener noreferrer\"><em><strong>Policitemia Rubra Vera<\/strong> <\/em><\/a><br \/>\nMKB D45<br \/>\nPolycythemia Rubra Vera<br \/>\nKjo gjendje shfaqet kur palca e kock\u00ebs prodhon s\u00eb tep\u00ebrmi eritrocite. Mbi 90% prej tyre jan\u00eb t\u00eb prekur me mutacion gjeni, i quajtur gjeni JAK 2 , i cili supozohet se nuk shkakton direkt PV, por e rrit rrezikun p\u00ebr shfaqjen e saj. Policitemia vera \u00ebsht\u00eb e rrall\u00eb dhe kryesisht prek personat pas t\u00eb 60-ve. Karakteristike \u00ebsht\u00eb fytyra e kuqe, shkaktuar nga koncentrimi i madh i eritrociteve , ndonj\u00ebher\u00eb i keqinterpretuar si irritim q\u00eb shfaqet gjat\u00eb konsumimit t\u00eb alkoolit.<\/p>\n<p>Simptomat<br \/>\nMeqen\u00ebse zhvillohet ngadal\u00eb, pacienti \u00ebsht\u00eb bart\u00ebs i k\u00ebsaj s\u00ebmundje me vite, pa v\u00ebrejtur asnj\u00ebfar\u00eb shenje apo simptoma tek shum\u00eb pacient\u00eb Policitemia vera madje nuk mund t\u00eb shkaktoj\u00eb asnj\u00eb lloj shenje apo simptome. Gjithsesi disa njer\u00ebz mund t\u00eb ndiejn\u00eb problemet e m\u00ebposhtme:<br \/>\nTension i lart\u00eb i gjakut<br \/>\nDhimbje koke dhe shikim i mjegulluar<br \/>\nTrullosje<br \/>\nDeboles\u00eb<br \/>\nDjersitje e tepruar<br \/>\nShqet\u00ebsime n\u00eb stomak<br \/>\n\u00cbnjtje me dhimbje t\u00eb ky\u00e7it, zakonisht tek gishti i madh i k\u00ebmb\u00ebs<br \/>\nFrym\u00ebmarrje e r\u00ebnduar kur pacienti shtrihet<br \/>\nNg\u00ebr\u00e7<br \/>\nNdjesi mbingopje dhe lodhje n\u00eb pjes\u00ebn e sip\u00ebrme t\u00eb abdomenit, p\u00ebr shkak t\u00eb zmadhimit t\u00eb shpretk\u00ebs<br \/>\nL\u00ebkur\u00eb e kuqe, sidomos n\u00eb pjes\u00ebn e fytyr\u00ebs, duarve dhe thembrave<br \/>\nProbleme me gjakderdhjen \u2013 nga hunda dhe krijimin e shpejt\u00eb t\u00eb mavijosjeve<br \/>\nGiht, q\u00eb mund t\u00eb shkaktoj\u00eb dhimbe n\u00eb ky\u00e7e, ng\u00ebr\u00e7 dhe \u00ebnjtje<\/p>\n<p>Policitemia rubra vera shfaqet kur mutacioni n\u00eb qelizat e palc\u00ebs s\u00eb kock\u00ebs shkakton probleme t\u00eb lidhura me prodhimin e qelizave t\u00eb gjakut. N\u00eb kushte normale trupi e rregullon me kujdes numrin e secilit prej tre tipave t\u00eb qelizave t\u00eb gjakut. Gjithsesi, tek Policitemia vera ky mekaniz\u00ebm rregullues \u00ebsht\u00eb i d\u00ebmtuar dhe palca e kock\u00ebs prodhon me shum\u00eb qeliza gjaku nga nj\u00eb tip. Shumica e personave t\u00eb prekur me Policitemia vera kan\u00eb nj\u00eb lloj t\u00eb till\u00eb mutacioni. Shkaku i saj nuk \u00ebsht\u00eb i qart\u00eb, por shkenc\u00ebtar\u00ebt besojn\u00eb se ajo shfaqet pas mbarsjes, k\u00ebshtu pra q\u00eb mund t\u00eb thuhet se nuk \u00ebsht\u00eb e fituar dhe nuk \u00ebsht\u00eb \u00e7rregullim i trash\u00ebguar nga prindi.<br \/>\nKurimi bazohet tek flebotomia (heqja e shpesht\u00eb e gjakut), p\u00ebr p\u00ebrmir\u00ebsimin e qarkullimit t\u00eb gjakut. Tek pacient\u00eb me rrezik t\u00eb shtuar p\u00ebr tromboz\u00eb, p\u00ebr shkak t\u00eb mosh\u00ebs s\u00eb tyre mbi 60-t\u00eb vje\u00e7, duhet t\u00eb merret parasysh edhe ekzistenca e nj\u00eb tromboze t\u00eb m\u00ebparshme, s\u00ebmundje periferike vaskulare ose hipertension, citoradukasion. \u201eHidroksiurea\u201e mbetet edhe medikamenti referent p\u00ebr pacient\u00ebt m\u00eb t\u00eb moshuar. Tek ato q\u00eb nuk kan\u00eb kontraindikacione t\u00eb ve\u00e7anta, \u00ebsht\u00eb v\u00ebrtetuar se \u201eAspirina\u201e n\u00eb doza t\u00eb vogla e redukton rrezikun nga tromboza. Kurimi me \u201eInterferon alfa\u201e mund t\u00eb sugjerohet tek shtatz\u00ebnat ose pacientet me mosh\u00eb m\u00eb t\u00eb re. Pasi q\u00eb shumica e pacient\u00ebve kan\u00eb mutacionin e gjenit JAK 2, rekomandohet edhe p\u00ebrdorimi i inhibitor\u00ebve t\u00eb JAK.<\/p>\n<p>Simptomat jan\u00eb t\u00eb lidhura me hiperviskozitetin e gjakut, p\u00ebr shkak t\u00eb rritjes s\u00eb numrit t\u00eb qelizave t\u00eb kuqe t\u00eb gjakut. Kjo gj\u00eb e \u00e7rregullon mikroqarkullimin. Simptomat jan\u00eb shpesh tin\u00ebzake n\u00eb fillim dhe mund t\u00eb p\u00ebrfshijn\u00eb dhimbje koke, marramendje, vertigo, tinitus, \u00e7rregullime n\u00eb shikim dhe pruritus pas larjes, ton t\u00eb p\u00ebrflakur q\u00eb shfaqet n\u00eb fytyr\u00eb, p\u00ebll\u00ebmb\u00eb, thonj, mukoz\u00eb dhe konjunktiv\u00eb.<br \/>\nKomplikimet mund t\u00eb jen\u00eb t\u00eb lidhura, krahas t\u00eb tjerave me tromboz\u00eb arteriale (n\u00eb rajonin cerebrovaskular, miokardik ose periferik), angina pektoris ose klaudikacione t\u00eb alternuara ose tromboz\u00eb venoze, duke p\u00ebrfshir\u00eb edhe tromboz\u00ebn e thell\u00eb venoze, embolin\u00eb pulmonare, tromboz\u00ebn e gj\u00ebndrave spilanoze) dhe gjakderdhjen, duke p\u00ebrfshir\u00eb gjakderdhjen e qiellz\u00ebs, ekhimozat dhe gjakderdhjen gastrointestinale .<br \/>\nPV mund t\u00eb karakterizohet edhe me splenomegali. Disa prej pacient\u00ebve mund t\u00eb zhvillojn\u00eb edhe mielofibroz\u00eb dhe leukemi akute ose sindrom\u00ebn mielodiplastike, q\u00eb shfaqet tek nj\u00eb num\u00ebr shum\u00eb i vog\u00ebl pacient\u00ebsh, zakonisht n\u00eb faz\u00ebn e avancuar t\u00eb s\u00ebmundjes.<br \/>\nPasi q\u00eb PV \u00ebsht\u00eb nj\u00eb lloj i rrall\u00eb i karcinomit t\u00eb gjakut, diagnoza zakonisht jepet kur pacienti vizitohet tek doktori p\u00ebr shkaqe t\u00eb tjera. Q\u00eb t\u00eb diagnostifikohet PV, b\u00ebhet testi i gjakut dhe analiza e palc\u00ebs s\u00eb kock\u00ebs.<\/p>\n\n<div style=\"font-size: 0px; height: 0px; line-height: 0px; margin: 0; padding: 0; clear: both;\"><\/div>","protected":false},"excerpt":{"rendered":"<p>Policitemia Rubra Vera MKB D45 Polycythemia Rubra Vera Kjo gjendje shfaqet kur palca e kock\u00ebs prodhon s\u00eb tep\u00ebrmi eritrocite. Mbi [&hellip;]<\/p>\n","protected":false},"author":24,"featured_media":107429,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_mo_disable_npp":"","inline_featured_image":false},"categories":[1794],"tags":[],"imageURL":"https:\/\/sdk.mk\/wp-content\/uploads\/2020\/02\/22-Polycythemia-Rubra-Vera-650x366.png","thumbURL":"https:\/\/sdk.mk\/wp-content\/uploads\/2020\/02\/22-Polycythemia-Rubra-Vera-250x141.png","categoryNames":["Uncategorized"],"feature_caption":"","subtitle":"","views":"17755","source":"\u0421\u043a\u043e\u043f\u0458\u0435, (\u0421\u0410\u041a\u0410\u041c\u0414\u0410\u041a\u0410\u0416\u0410\u041c.\u041c\u041a)","yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v15.0 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>JU NJOFTOJM\u00cb ME S\u00cbMUNDJET E RRALLA: POLICITEMIA RUBRA VERA - \u0421\u0430\u043a\u0430\u043c \u0414\u0430 \u041a\u0430\u0436\u0430\u043c<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/sdk.mk\/index.php\/uncategorized-sq\/ju-njoftojme-me-semundjet-e-rralla-policitemia-rubra-vera\/\" \/>\n<meta property=\"og:locale\" content=\"mk_MK\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"JU NJOFTOJM\u00cb ME S\u00cbMUNDJET E RRALLA: POLICITEMIA RUBRA VERA - \u0421\u0430\u043a\u0430\u043c \u0414\u0430 \u041a\u0430\u0436\u0430\u043c\" \/>\n<meta property=\"og:description\" content=\"Policitemia Rubra Vera MKB D45 Polycythemia Rubra Vera Kjo gjendje shfaqet kur palca e kock\u00ebs prodhon s\u00eb tep\u00ebrmi eritrocite. 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