{"id":138617,"date":"2021-02-09T17:23:25","date_gmt":"2021-02-09T16:23:25","guid":{"rendered":"https:\/\/sdk.mk\/?p=138617"},"modified":"2021-02-09T17:23:25","modified_gmt":"2021-02-09T16:23:25","slug":"ju-njoftojme-me-semundjet-e-rralla-semundja-karoli","status":"publish","type":"post","link":"https:\/\/sdk.mk\/index.php\/uncategorized-sq\/ju-njoftojme-me-semundjet-e-rralla-semundja-karoli\/","title":{"rendered":"JU NJOFTOJM\u00cb ME S\u00cbMUNDJET E RRALLA: S\u00cbMUNDJA KAROLI"},"content":{"rendered":"<div class=\"f52428582a4b906b2d2e2a7d733c7d27\" data-index=\"7\" style=\"float: none; margin:10px 0 10px 0; text-align:center;\">\n<!-- MSP Ads Asynchronous JS Tag - Generated with Revive Adserver v5.4.1 -->\r\n<ins data-revive-zoneid=\"167\" data-revive-id=\"060fdb01f6430ec164d3519234aa4967\"><\/ins>\r\n<script async src=\"\/\/panel.ads.com.mk\/www\/delivery\/asyncjs.php\"><\/script>\n<\/div>\n<p><a href=\"https:\/\/www.youtube.com\/watch?v=xq3S-gSuKNQ&amp;list=PLPGcigDEy-qjbp5PqAn9GhcRLTEx3PuVd&amp;index=9\" target=\"_blank\" rel=\"noopener noreferrer\"><em><strong>Caroli disease &#8211; S\u00ebmundja Karoli<\/strong><\/em><\/a><br \/>\nICD Q 44.6<br \/>\nPrevalenca: e panjohur<\/p>\n<p>S\u00ebmudnja Karoli \u00ebsht\u00eb s\u00ebmundje e rrall\u00eb e lindur e m\u00ebl\u00e7is\u00eb. Shfaqet si rezultat i zgjerimit t\u00eb kanaleve biliare t\u00eb vendosura n\u00eb m\u00ebl\u00e7i. Qarkullimi normal i vrerit \u00ebsht\u00eb i \u00e7rregulluar dhe vjen gjer te stagnimi i vrerit i cili si pasoj\u00eb zhvillon infeksionin. S\u00ebmundja shfaqet m\u00eb shpesh tek meshkujt, n\u00eb f\u00ebmij\u00ebri ose adoleshenc\u00ebn e hershme. Zhvillimi i s\u00ebmundjes varet drejtp\u00ebrdrejt nga shkalla e d\u00ebmtimit t\u00eb kanaleve t\u00eb m\u00ebl\u00e7is\u00eb.<\/p>\n<p>Trash\u00ebgimi:<\/p>\n<p>S\u00ebmudnja Karoli trash\u00ebgohet n\u00eb m\u00ebnyr\u00eb autosomale recisive. N\u00ebse n\u00eb familje ka t\u00eb af\u00ebrm me nj\u00eb patologji t\u00eb ngjashme, at\u00ebher\u00eb duhet b\u00ebr\u00eb nj\u00eb ekzaminim i detajuar menj\u00ebher\u00eb pas lindjes s\u00eb f\u00ebmij\u00ebs, pasi ekziston nj\u00eb rrezik i trash\u00ebgimit t\u00eb s\u00ebmundjes.<\/p>\n<p>Format e s\u00ebmundjes Karoli:<\/p>\n<p>Ende nuk ka nj\u00eb klasifikim specifik t\u00eb s\u00ebmundjes Karoli. Sidoqoft\u00eb, ekzistojn\u00eb dy forma t\u00eb ndryshme t\u00eb s\u00ebmundjes. Forma e par\u00eb karakterizohet nga fakti se p\u00ebrshkueshm\u00ebria e kanaleve biliare \u00ebsht\u00eb e kapur, dhe si pasoj\u00eb formohen gur\u00ebt e t\u00ebmthit. Forma e dyt\u00eb shoq\u00ebrohet me fibroz\u00eb kongjenitale t\u00eb m\u00ebl\u00e7is\u00eb (akumulimi i indit lidh\u00ebs n\u00eb m\u00ebl\u00e7i). N\u00eb k\u00ebt\u00eb rast, ekziston nj\u00eb zgjerim i leht\u00eb i kanaleve, nuk formohen gur\u00eb, megjith\u00ebse ato ndonj\u00ebher\u00eb mund edhe t\u00eb formohen n\u00eb fazat e m\u00ebvonshme t\u00eb s\u00ebmundjes.<\/p>\n<p>Simptomat:<\/p>\n<p>Simptomat e s\u00ebmundjes Karoli mund t\u00eb shfaqen tek f\u00ebmij\u00ebt dhe t\u00eb rinjt\u00eb e \u00e7do moshe. Shenjat kryesore t\u00eb s\u00ebmundjes jan\u00eb:<\/p>\n<p>* dhimbje barku;<br \/>\n* ethe;<br \/>\n* ikter (zverdhje e l\u00ebkur\u00ebs);<br \/>\n* zmadhimi i m\u00ebl\u00e7is\u00eb.<\/p>\n<p>Manifestimet e theksuara klinike t\u00eb s\u00ebmundjes shpesh shoq\u00ebrohen me p\u00ebrparim t\u00eb procesit inflamator. Progresioni i s\u00ebmundjes rezulton me nj\u00eb rritje t\u00eb konsiderueshme t\u00eb nivelit t\u00eb bilirubin\u00ebs dhe leukociteve n\u00eb gjak.<\/p>\n<p>Diagnostikimi:<\/p>\n<p>Edhe pse simptomat e s\u00ebmundjes jan\u00eb shum\u00eb t\u00eb theksuara, ato jan\u00eb karakteristike edhe p\u00ebr shum\u00eb s\u00ebmundje t\u00eb tjera t\u00eb m\u00ebl\u00e7is\u00eb. Diagnoza e s\u00ebmundjes mund t\u00eb b\u00ebhet me an\u00eb t\u00eb ultraz\u00ebrit dhe tomografis\u00eb, dhe n\u00ebse \u00ebsht\u00eb e nevojshme edhe me kolangiografi endoskopike.<br \/>\nTestet e funksionit t\u00eb m\u00ebl\u00e7is\u00eb nuk \u00e7rregullohen p\u00ebr nj\u00eb koh\u00eb t\u00eb gjat\u00eb, por me p\u00ebrparimin e s\u00ebmundjes dhe nj\u00eb procesi inflamator t\u00eb zgjatur, mund t\u00eb zbulohen t\u00eb gjitha shenjat e kolestaz\u00ebs. P\u00ebr shkak se pacient\u00ebt jan\u00eb n\u00eb rrezik p\u00ebr shfaqjen e kancerit, prandaj duhen t\u00eb testohet prezenca e tumor marker\u00ebve.<\/p>\n<p>Trajtimi:<\/p>\n<p>Trajtimi p\u00ebrfshin p\u00ebrdorimin e antibiotik\u00ebve me spekt\u00ebr t\u00eb gjer\u00eb, si dhe acidin ursodeoksikolik p\u00ebr t\u00eb parandaluar formimin e gur\u00ebve.<br \/>\nGjithashtu trajtimi p\u00ebrfshin:<br \/>\nAnelgjetik\u00eb<br \/>\nHeqja e gur\u00ebve<br \/>\nDrenazh i t\u00ebmthit<br \/>\nOperacioni kryhet vet\u00ebm n\u00eb p\u00ebrkeq\u00ebsime t\u00eb shpeshta t\u00eb gjendjes s\u00eb pacientit ose kur p\u00ebrdorimi i metodave konservative t\u00eb trajtimit nuk kan\u00eb efekt. N\u00ebse kanalet biliare jan\u00eb shum\u00eb t\u00eb zgjeruara dhe vreri nuk qarkullon, mund t\u00eb hiqet nj\u00eb lob i m\u00ebl\u00e7is\u00eb. N\u00eb raste ve\u00e7an\u00ebrisht t\u00eb r\u00ebnda t\u00eb insufi\u00e7ienc\u00ebs hepatike ose zhvillimit t\u00eb kancerit, rekomandohet nj\u00eb transplantim i m\u00ebl\u00e7is\u00eb. Prognoza e k\u00ebsaj s\u00ebmundje \u00ebsht\u00eb e pafavorshme p\u00ebr shkak t\u00eb relapsit dhe ndonj\u00ebher\u00eb vjen gjer te vdekja e pacientit.<\/p>\n<p>Sindroma Karoli:<\/p>\n<p>S\u00ebmundja Karoli shpesh lidhet me fibroz\u00eb kongjenitale t\u00eb m\u00ebl\u00e7is\u00eb q\u00eb vjen nga \u00e7rregullime pothuajse identike gjat\u00eb formimit t\u00eb kanaleve biliare n\u00eb stadin embrional; e cila \u00ebsht\u00eb nj\u00eb gjendje e referuar si sindroma Karoli.<\/p>\n<p>Sindroma Karoli manifestohet nga dhimbje barku, si dhe me gjakderdhje nga venat me vari\u00e7e t\u00eb ezofagut. Tek neonat\u00ebt mund t\u00eb paraqitet si kombinim i simptomave kryesore t\u00eb fibroz\u00ebs kongjenitale t\u00eb m\u00ebl\u00e7is\u00eb, s\u00ebmundjes Karoli dhe s\u00ebmundjes polikistike t\u00eb veshkave. N\u00eb vitet e para, patologjia \u00ebsht\u00eb pothuajse asimptomatike, gjersa dilatimi i kanaleve biliare shkakton ngecje biliare, duke \u00e7uar n\u00eb formimin e gur\u00ebve dhe zhvillimin e infeksionit. Kryesisht d\u00ebmtimi i m\u00ebl\u00e7is\u00eb zhvillohet n\u00eb an\u00ebn e majt\u00eb, megjith\u00ebse n\u00eb disa raste mund t\u00eb p\u00ebrfshij\u00eb t\u00ebr\u00eb organin. Nj\u00eb nga nd\u00ebrlikimet mund t\u00eb jet\u00eb zhvillimi i insufi\u00e7ienc\u00ebs renale.<\/p>\n\n<div style=\"font-size: 0px; height: 0px; line-height: 0px; margin: 0; padding: 0; clear: both;\"><\/div>","protected":false},"excerpt":{"rendered":"<p>Caroli disease &#8211; S\u00ebmundja Karoli ICD Q 44.6 Prevalenca: e panjohur S\u00ebmudnja Karoli \u00ebsht\u00eb s\u00ebmundje e rrall\u00eb e lindur e [&hellip;]<\/p>\n","protected":false},"author":24,"featured_media":138615,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_mo_disable_npp":"no","inline_featured_image":false},"categories":[1794],"tags":[],"imageURL":"https:\/\/sdk.mk\/wp-content\/uploads\/2021\/02\/09-Karolieva-bolest-650x366.png","thumbURL":"https:\/\/sdk.mk\/wp-content\/uploads\/2021\/02\/09-Karolieva-bolest-250x141.png","categoryNames":["Uncategorized"],"feature_caption":"","subtitle":"","views":"359","source":"\u0421\u043a\u043e\u043f\u0458\u0435, (\u0421\u0410\u041a\u0410\u041c\u0414\u0410\u041a\u0410\u0416\u0410\u041c.\u041c\u041a)","yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v15.0 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>JU NJOFTOJM\u00cb ME S\u00cbMUNDJET E RRALLA: S\u00cbMUNDJA KAROLI - \u0421\u0430\u043a\u0430\u043c \u0414\u0430 \u041a\u0430\u0436\u0430\u043c<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/sdk.mk\/index.php\/uncategorized-sq\/ju-njoftojme-me-semundjet-e-rralla-semundja-karoli\/\" \/>\n<meta property=\"og:locale\" content=\"mk_MK\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"JU NJOFTOJM\u00cb ME S\u00cbMUNDJET E RRALLA: S\u00cbMUNDJA KAROLI - \u0421\u0430\u043a\u0430\u043c \u0414\u0430 \u041a\u0430\u0436\u0430\u043c\" \/>\n<meta property=\"og:description\" content=\"Caroli disease &#8211; 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