{"id":165070,"date":"2022-02-01T10:59:33","date_gmt":"2022-02-01T09:59:33","guid":{"rendered":"https:\/\/sdk.mk\/?p=165070"},"modified":"2022-02-02T09:15:52","modified_gmt":"2022-02-02T08:15:52","slug":"ju-njoftojme-me-semundjet-e-rralla-sindroma-gillian-barre","status":"publish","type":"post","link":"https:\/\/sdk.mk\/index.php\/maqedonia\/ju-njoftojme-me-semundjet-e-rralla-sindroma-gillian-barre\/","title":{"rendered":"JU NJOFTOJM\u00cb ME S\u00cbMUNDJET E RRALLA: SINDROMA GILLIAN-BARRE"},"content":{"rendered":"<div class=\"f52428582a4b906b2d2e2a7d733c7d27\" data-index=\"7\" style=\"float: none; margin:10px 0 10px 0; text-align:center;\">\n<!-- MSP Ads Asynchronous JS Tag - Generated with Revive Adserver v5.4.1 -->\r\n<ins data-revive-zoneid=\"167\" data-revive-id=\"060fdb01f6430ec164d3519234aa4967\"><\/ins>\r\n<script async src=\"\/\/panel.ads.com.mk\/www\/delivery\/asyncjs.php\"><\/script>\n<\/div>\n<p><strong><span lang=\"mk-MK\">Sindroma Gillian-Barre\/Guillain-Barr\u00e9 syndrome<\/span><\/strong><\/p>\n<p lang=\"mk-MK\">ICD: G 61.0<\/p>\n<p lang=\"mk-MK\">Prevalenca: 1-9\/100.000<\/p>\n<p lang=\"mk-MK\">Sindroma Gillian-Barre \u00ebsht\u00eb nj\u00eb \u00e7rregullim neurologjik n\u00eb t\u00eb cilin sistemi imunitar sulmon indet e veta t\u00eb sistemit nervor periferik. S\u00ebmundja u p\u00ebrshkrua p\u00ebr her\u00eb t\u00eb par\u00eb n\u00eb 1859 nga mjeku francez Zhan Landri, nd\u00ebrsa n\u00eb 1916, Xhorxh Gillian, Zhan Aleksand\u00ebr Barre dhe Andr\u00e9 diagnostikuan s\u00ebmundjen te dy ushtar\u00eb dhe zbuluan nj\u00eb anomali t\u00eb madhe &#8211; rritjen e prodhimit t\u00eb proteinave n\u00eb l\u00ebngun cerebrospinal, megjith\u00ebse numri i qelizave mbeti normal.<\/p>\n<p lang=\"mk-MK\">S\u00ebmundja mund t\u00eb zhvillohet n\u00eb disa or\u00eb ose dit\u00eb, por zakonisht zhvillohet n\u00eb disa jav\u00eb. Dob\u00ebsia e muskujve \u00ebsht\u00eb e zakonshme n\u00eb dy jav\u00ebt e para pas shfaqjes s\u00eb simptomave, dhe deri n\u00eb fund t\u00eb jav\u00ebs s\u00eb tret\u00eb, 90% e pacient\u00ebve p\u00ebrjetojn\u00eb dob\u00ebsin\u00eb m\u00eb t\u00eb madhe t\u00eb muskujve. Sindroma Gillian-Barre takon n\u00eb nj\u00eb grup \u00e7rregullimesh autoimune n\u00eb t\u00eb cilat trupi nuk njeh indet e veta.<\/p>\n<p lang=\"mk-MK\">K\u00ebll\u00ebfi i mielin\u00ebs q\u00eb mb\u00ebshtjell nervat \u00ebsht\u00eb sh\u00ebnjestra kryesore e antitrupave. Kur mb\u00ebshtjell\u00ebsi i mielin\u00ebs d\u00ebmtohet ose shkat\u00ebrrohet, nervat nuk mund t\u00eb transmetojn\u00eb sinjale dhe muskujt humbasin aft\u00ebsin\u00eb p\u00ebr t\u00eb reaguar. N\u00eb m\u00ebnyr\u00eb t\u00eb barabart\u00eb, truri merr m\u00eb pak informacion p\u00ebr pjes\u00ebn tjet\u00ebr t\u00eb trupit, t\u00eb gjitha k\u00ebto rezultojn\u00eb n\u00eb nj\u00eb paaft\u00ebsi p\u00ebr t\u00eb ndjer\u00eb prekjen, temperatur\u00ebn, dhimbjen, etj.<\/p>\n<p lang=\"mk-MK\">Fatkeq\u00ebsisht, shkaku i sakt\u00eb i sindrom\u00ebs Gillian-Barre nuk \u00ebsht\u00eb kuptuar plot\u00ebsisht. N\u00ebse s\u00ebmundja \u00ebsht\u00eb paraprir\u00eb nga nj\u00eb infeksion, \u00ebsht\u00eb e mundur q\u00eb sistemi imunitar t\u00eb njoh\u00eb mb\u00ebshtjell\u00ebs\u00ebn e mielin\u00ebs si nj\u00eb trup t\u00eb huaj dhe ta sulmoj\u00eb at\u00eb. Gjithashtu \u00ebsht\u00eb e mundur q\u00eb viruset t\u00eb d\u00ebmtojn\u00eb aft\u00ebsin\u00eb e sistemit imunitar p\u00ebr t\u00eb dalluar indet e veta nga t\u00eb huajat.<\/p>\n<p lang=\"mk-MK\">Ky sindrom prek njer\u00ebzit e t\u00eb gjitha moshave dhe gjinive n\u00eb m\u00ebnyr\u00eb t\u00eb barabart\u00eb. \u00c7rregullimi zakonisht shfaqet disa dit\u00eb ose nj\u00eb jav\u00eb pasi pacienti ka patur simptoma t\u00eb infeksionit. Ndonj\u00ebher\u00eb shtatz\u00ebnia, operacioni ose vaksinimi mund t&#8217;i paraprijn\u00eb sindrom\u00ebs. Megjith\u00ebse fillimi i k\u00ebsaj s\u00ebmundjeje \u00ebsht\u00eb i papritur, sh\u00ebrimi nuk \u00ebsht\u00eb i shpejt\u00eb. Rreth 30% e pacient\u00ebve ndihen ende t\u00eb dob\u00ebt pas tre vjet\u00ebsh, dhe 3-5% e pacient\u00ebve mund t\u00eb kthejn\u00eb forc\u00ebn e muskujve shum\u00eb vite pas sulmit t\u00eb par\u00eb.<\/p>\n<p><strong><span lang=\"mk-MK\">Simptomat:<\/span><\/strong><\/p>\n<p lang=\"mk-MK\">Simptomat e para p\u00ebrfshijn\u00eb dob\u00ebsi n\u00eb k\u00ebmb\u00eb me intensitet t\u00eb ndrysh\u00ebm, dhe k\u00ebto ndjenja ndonj\u00ebher\u00eb p\u00ebrhapen n\u00eb pjes\u00ebn e sip\u00ebrme t\u00eb trupit dhe krah\u00ebve. Simptomat e m\u00ebposhtme zakonisht shfaqen t\u00eb parat:<\/p>\n<p>\u2022 <span lang=\"mk-MK\">muskujt nuk mund t\u00eb l\u00ebvizin fare;<\/span><\/p>\n<p>\u2022 <span lang=\"mk-MK\">pacienti b\u00ebhet pothuajse i paralizuar;<\/span><\/p>\n<p>\u2022 <span lang=\"mk-MK\">mund t\u00eb ket\u00eb v\u00ebshtir\u00ebsi n\u00eb frym\u00ebmarrje;<\/span><\/p>\n<p>\u2022 <span lang=\"mk-MK\">pacienti nuk reagon ndaj ndryshimeve t\u00eb temperatur\u00ebs, si\u00e7 \u00ebsht\u00eb temperatura e ujit gjat\u00eb dushit, dhe mund t\u00eb ndodhin djegie.<\/span><\/p>\n<p><strong><span lang=\"mk-MK\">Diagnoza:<\/span><\/strong><\/p>\n<p lang=\"mk-MK\">Sindroma \u00ebsht\u00eb nj\u00eb term mjek\u00ebsor p\u00ebr nj\u00eb grup simptomash q\u00eb ndjen nj\u00eb pacient dhe shenja q\u00eb v\u00ebren nga mjeku. Shenjat dhe simptomat e sindrom\u00ebs mund t\u00eb ndryshojn\u00eb n\u00eb m\u00ebnyr\u00eb t\u00eb konsiderueshme nga pacienti n\u00eb pacient, k\u00ebshtu q\u00eb \u00ebsht\u00eb e v\u00ebshtir\u00eb p\u00ebr mjek\u00ebt q\u00eb n\u00eb disa raste ta njohin k\u00ebt\u00eb sindrom\u00eb n\u00eb nj\u00eb faz\u00eb t\u00eb hershme. Shum\u00eb \u00e7rregullime t\u00eb tjera gjithashtu kan\u00eb simptoma t\u00eb ngjashme.<\/p>\n<p lang=\"mk-MK\">Shenjat dhe simptomat q\u00eb mund ta dallojn\u00eb sindrom\u00ebn Gillian-Barre nga \u00e7rregullimet e tjera p\u00ebrfshijn\u00eb:<\/p>\n<ul>\n<li>\n<p lang=\"mk-MK\">simptomat shfaqen n\u00eb t\u00eb dy an\u00ebt e trupit brenda pak dit\u00ebsh;<\/p>\n<\/li>\n<li>\n<p lang=\"mk-MK\">reflekset humbasin;<\/p>\n<\/li>\n<li>\n<p lang=\"mk-MK\">l\u00ebngu cerebrospinal (CSF) p\u00ebrmban m\u00eb shum\u00eb proteina se zakonisht.<\/p>\n<\/li>\n<\/ul>\n<p lang=\"mk-MK\">Diagnoza e sakt\u00eb k\u00ebrkon nj\u00eb ekzaminim t\u00eb holl\u00ebsish\u00ebm nga nj\u00eb neurolog. Nj\u00eb test gjaku me nj\u00eb k\u00ebrkim t\u00eb detajuar t\u00eb autoantitrupave \u00ebsht\u00eb nj\u00eb faktor shum\u00eb i r\u00ebnd\u00ebsish\u00ebm. EMG (elektromioneurografia) tregon nj\u00eb reduktim t\u00eb p\u00ebrcjellshm\u00ebris\u00eb nervore dhe p\u00ebrdoret gjithnj\u00eb e m\u00eb shum\u00eb p\u00ebr t\u00eb p\u00ebrcaktuar shkall\u00ebn e d\u00ebmtimit dhe p\u00ebr t\u00eb vendosur nj\u00eb pik\u00eb referimi p\u00ebr terapi.<\/p>\n<p><strong><span lang=\"mk-MK\">Trajtimi:<\/span><\/strong><\/p>\n<p lang=\"mk-MK\">Fatkeq\u00ebsisht, nuk ka sh\u00ebrim p\u00ebr sindrom\u00ebn Gillian-Barre. Sidoqoft\u00eb, ekziston nj\u00eb terapi q\u00eb zvog\u00eblon ashp\u00ebrsin\u00eb e s\u00ebmundjes. Plazmafereza (shk\u00ebmbimi i plazm\u00ebs) dhe doza t\u00eb larta t\u00eb imunoglobulin\u00ebs p\u00ebrdoren n\u00eb raste t\u00eb r\u00ebnda t\u00eb k\u00ebtij sindromi. Trajtimi zakonisht konsiston n\u00eb zvog\u00eblimin e simptomave derisa t\u00eb ndodh\u00eb rikuperimi. Si nj\u00eb respirator ashtu edhe trajtimi n\u00eb nj\u00ebsin\u00eb e kujdesit intensiv mund t\u00eb ndihmojn\u00eb. Sapo pacienti fillon t\u00eb b\u00ebhet m\u00eb mir\u00eb, ai duhet t\u00eb filloj\u00eb terapi fizike. Ndryshimet mendore te pacient\u00ebt me k\u00ebt\u00eb sindrom\u00eb jan\u00eb t\u00eb zakonshme. Pacienti \u00ebsht\u00eb shpesh n\u00eb depresion dhe nervoz, dhe ka nevoj\u00eb p\u00ebr trajtim t\u00eb p\u00ebrshtatsh\u00ebm p\u00ebr t\u00eb gjitha k\u00ebto simptoma shoq\u00ebruese.<\/p>\n<p><strong><span lang=\"mk-MK\">Prognoza:<\/span><\/strong><\/p>\n<p lang=\"mk-MK\">N\u00eb shumic\u00ebn e rasteve, sh\u00ebrimi fillon pas jav\u00ebs s\u00eb 4 -t\u00eb t\u00eb s\u00ebmundjes. P\u00ebraf\u00ebrsisht 80% e pacient\u00ebve sh\u00ebrohen plot\u00ebsisht brenda disa muajve deri n\u00eb nj\u00eb vit, por disa simptoma, t\u00eb tilla si arefleksia, mund t\u00eb vazhdojn\u00eb pas sh\u00ebrimit. P\u00ebraf\u00ebrsisht 5-10% e pacient\u00ebve mbesin me pasoja t\u00eb r\u00ebnda, m\u00eb t\u00eb zakonshmet prej t\u00eb cilave jan\u00eb d\u00ebmtimi i r\u00ebnd\u00eb aksonal motorik dhe senzorik me paaft\u00ebsi p\u00ebr t\u00eb rigjeneruar aksonet. Por kjo sindrom\u00eb ende konsiderohet nj\u00eb s\u00ebmundje e rrezikshme dhe vdekshm\u00ebria, pavar\u00ebsisht p\u00ebrmir\u00ebsimeve t\u00eb m\u00ebdha n\u00eb trajtim dhe kujdes t\u00eb avancuar, \u00ebsht\u00eb ende rreth 2-3% n\u00eb spitalet m\u00eb t\u00eb mira n\u00eb bot\u00eb. N\u00eb bot\u00eb n\u00eb p\u00ebrgjith\u00ebsi, vdekshm\u00ebria \u00ebsht\u00eb pak m\u00eb e lart\u00eb (rreth 4%), kryesisht p\u00ebr shkak t\u00eb munges\u00ebs s\u00eb shpesht\u00eb t\u00eb pajisjeve p\u00ebr t\u00eb mbajtur pacientin gjall\u00eb, ve\u00e7an\u00ebrisht ventilator\u00ebt q\u00eb mund t\u00eb jen\u00eb t\u00eb nevojsh\u00ebm n\u00eb disa raste ekstreme. Sidoqoft\u00eb, ekziston mund\u00ebsia q\u00eb m\u00eb von\u00eb, te 5-10% e pacient\u00ebve, s\u00ebmundja t\u00eb kthehet, dhe k\u00ebt\u00eb mjek\u00ebt e quajn\u00eb neuropati kronike inflamatore demielinizante.<\/p>\n\n<div style=\"font-size: 0px; height: 0px; line-height: 0px; margin: 0; padding: 0; clear: both;\"><\/div>","protected":false},"excerpt":{"rendered":"<p>Sindroma Gillian-Barre\/Guillain-Barr\u00e9 syndrome ICD: G 61.0 Prevalenca: 1-9\/100.000 Sindroma Gillian-Barre \u00ebsht\u00eb nj\u00eb \u00e7rregullim neurologjik n\u00eb t\u00eb cilin sistemi imunitar sulmon [&hellip;]<\/p>\n","protected":false},"author":22,"featured_media":165179,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_mo_disable_npp":"no","inline_featured_image":false},"categories":[3087],"tags":[56776],"imageURL":"https:\/\/sdk.mk\/wp-content\/uploads\/2022\/02\/01-Guillain-Barre-syndrome-650x366.png","thumbURL":"https:\/\/sdk.mk\/wp-content\/uploads\/2022\/02\/01-Guillain-Barre-syndrome-250x141.png","categoryNames":["Maqedonia"],"feature_caption":"","subtitle":"","views":"1582","source":"\u0421\u043a\u043e\u043f\u0458\u0435, (\u0421\u0410\u041a\u0410\u041c\u0414\u0410\u041a\u0410\u0416\u0410\u041c.\u041c\u041a)","yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v15.0 - 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