{"id":165330,"date":"2022-02-04T09:27:36","date_gmt":"2022-02-04T08:27:36","guid":{"rendered":"https:\/\/sdk.mk\/?p=165330"},"modified":"2022-02-04T09:27:36","modified_gmt":"2022-02-04T08:27:36","slug":"ju-njoftojme-me-semundjet-e-rralla-sindroma-melkersson-rosenthal","status":"publish","type":"post","link":"https:\/\/sdk.mk\/index.php\/maqedonia\/ju-njoftojme-me-semundjet-e-rralla-sindroma-melkersson-rosenthal\/","title":{"rendered":"JU NJOFTOJM\u00cb ME S\u00cbMUNDJET E RRALLA: SINDROMA MELKERSSON-ROSENTHAL"},"content":{"rendered":"<div class=\"f52428582a4b906b2d2e2a7d733c7d27\" data-index=\"7\" style=\"float: none; margin:10px 0 10px 0; text-align:center;\">\n<!-- MSP Ads Asynchronous JS Tag - Generated with Revive Adserver v5.4.1 -->\r\n<ins data-revive-zoneid=\"167\" data-revive-id=\"060fdb01f6430ec164d3519234aa4967\"><\/ins>\r\n<script async src=\"\/\/panel.ads.com.mk\/www\/delivery\/asyncjs.php\"><\/script>\n<\/div>\n<p class=\"western\" lang=\"mk-MK\"><em><strong>Sindroma Melkersson-Rosenthal\/Melkersson-Rosenthal syndrome<\/strong><\/em><\/p>\n<p class=\"western\" lang=\"mk-MK\">ICD: G 51.2<\/p>\n<p class=\"western\" lang=\"mk-MK\">Prevalenca: e panjohur<\/p>\n<p class=\"western\" lang=\"mk-MK\">Sindroma Melkerson-Rosenthal \u00ebsht\u00eb nj\u00eb \u00e7rregullim i rrall\u00eb neurologjik i karakterizuar nga nj\u00eb treshe simptomash q\u00eb p\u00ebrs\u00ebriten: edem\u00eb orofaciale, ve\u00e7an\u00ebrisht t\u00eb nj\u00ebr\u00ebs ose t\u00eb dy buz\u00ebve, paraliz\u00eb t\u00eb fytyr\u00ebs dhe \u00e7arje t\u00eb gjuh\u00ebs.<\/p>\n<p class=\"western\" lang=\"mk-MK\">Sindroma u p\u00ebrshkrua p\u00ebr her\u00eb t\u00eb par\u00eb n\u00eb vitin 1920 nga Ernest Gustav Melkersson te nj\u00eb pacient 35-vje\u00e7ar me edem\u00eb orofaciale dhe paraliz\u00eb faciale. Lidhshm\u00ebria e paraliz\u00ebs t\u00eb fytyr\u00ebs dhe gjuh\u00ebs s\u00eb \u00e7ar\u00eb u p\u00ebrshkrua n\u00eb 1931 nga Rosenthal.<\/p>\n<p class=\"western\" lang=\"mk-MK\">Simptomat fillestare shfaqen midis mosh\u00ebs 25 dhe 40 vje\u00e7. Grat\u00eb kan\u00eb predispozicion m\u00eb t\u00eb lart\u00eb se burrat (2:1), nd\u00ebrsa tek f\u00ebmij\u00ebt kjo sindrom\u00eb \u00ebsht\u00eb e rrall\u00eb. Tridhjet\u00eb raste jan\u00eb raportuar tek f\u00ebmij\u00ebt deri m\u00eb tani, me simptomat fillestare q\u00eb shfaqen midis mosh\u00ebs 7 dhe 12 vje\u00e7.<\/p>\n<p class=\"western\" lang=\"mk-MK\"><strong>Etiologjia:<\/strong><\/p>\n<p class=\"western\" lang=\"mk-MK\">Etiologjia e SMR \u00ebsht\u00eb e pasqaruar. Etiopatogjeneza e rasteve t\u00eb rralla pediatrike shoq\u00ebrohet me infeksion t\u00eb shkaktuar nga virusi Herpes Simplex, \u00e7rregullime t\u00eb trash\u00ebguara granulomatoze, tuberkulozi dhe lebra, infeksione kronike, sindroma Daun, psoriaza, tiroiditi, skleroza multiple, keratiti, Wegener granulomatoza, diabeti, sarkoidoza, koliti ulceroz dhe alergjit\u00eb. Infeksionet respirator\u00eb nga virusi i gripit mund te jen\u00eb n\u00eb faktor nxit\u00ebs p\u00ebr relaps t\u00eb s\u00ebmundjes.<\/p>\n<p class=\"western\" lang=\"mk-MK\">Ka prova q\u00eb sugjerojn\u00eb se sindroma Melkersson-Rosenthal ka faktor\u00eb trash\u00ebgues pasi q\u00eb trash\u00ebgimia familjare \u00ebsht\u00eb raportuar te disa pacient\u00eb. Sidoqoft\u00eb, paraqitja klinike ndryshon dhe e b\u00ebn procesin diagnostikues nj\u00eb lloj sfide p\u00ebr mjek\u00ebt.<\/p>\n<p class=\"western\" lang=\"mk-MK\"><strong>Simptomat:<\/strong><\/p>\n<p class=\"western\" lang=\"mk-MK\">Sindroma Melkersson-Rosenthal zakonisht definohet nga triada klasike e simptomave (paraliza e fytyr\u00ebs, edema orofaciale e p\u00ebrs\u00ebritur dhe gjuha e \u00e7ar\u00eb). Paraqitja e plot\u00eb klinike e saj \u00ebsht\u00eb e pazakont\u00eb. Ajo p\u00ebrshkruhet n\u00eb vet\u00ebm 10-25% t\u00eb rasteve t\u00eb diagnostikuara.<\/p>\n<p class=\"western\" lang=\"mk-MK\">Paraliza faciale<\/p>\n<p class=\"western\" lang=\"mk-MK\">Paraliza e fytyr\u00ebs ka nj\u00eb origjin\u00eb neurologjike dhe karakterizohet nga pal\u00ebvizshm\u00ebria e muskujve q\u00eb inervohen nga nervi facial. Kjo gjendje m\u00eb shpesh ndodh si rezultat i d\u00ebmtimit t\u00eb p\u00ebrkohsh\u00ebm ose t\u00eb p\u00ebrhersh\u00ebm t\u00eb nervit, e shkaktuar nga inflamacioni, d\u00ebmtimi i indeve, etj.<\/p>\n<p class=\"western\" lang=\"mk-MK\">Nervi facial \u00ebsht\u00eb p\u00ebrgjegj\u00ebs p\u00ebr inervimin e zonave t\u00eb ndryshme t\u00eb fytyr\u00ebs dhe strukturave p\u00ebrreth. Funksioni i tij \u00ebsht\u00eb t\u00eb kontrolloj\u00eb shprehjet e fytyr\u00ebs q\u00eb lejojn\u00eb shprehjen e emocioneve, artikulimin e z\u00ebrave, tingujve, t\u00eb ushqyerit etj. Prania e proceseve t\u00eb ndryshme patologjike mund t\u00eb shkaktoj\u00eb dob\u00ebsim ose paraliz\u00eb t\u00eb zon\u00ebs q\u00eb kontrollon nervi facial.<\/p>\n<p class=\"western\" lang=\"mk-MK\">Te SMR, paraliza e fytyr\u00ebs mund t\u00eb jet\u00eb periferike n\u00eb nj\u00ebr\u00ebn an\u00eb t\u00eb fytyr\u00ebs dhe me nj\u00eb karakter p\u00ebrs\u00ebrit\u00ebs. Kjo simptom\u00eb shfaqet te m\u00eb shum\u00eb se 30% t\u00eb pacient\u00ebve. Zakonisht zhvillohet shpejt, p\u00ebr rreth 24-48 or\u00eb.<\/p>\n<p class=\"western\" lang=\"mk-MK\">Edema orofaciale<\/p>\n<p class=\"western\" lang=\"mk-MK\">Edema orofaciale \u00ebsht\u00eb e pranishme n\u00eb 80% t\u00eb rasteve. Karakterizohet nga akumulimi patologjik i l\u00ebngut q\u00eb krijon inflamacion ose \u00ebnjtje n\u00eb zon\u00ebn e prekur. Mund ta p\u00ebrfshij\u00eb fytyr\u00ebn pjes\u00ebrisht ose plot\u00ebsisht, gjuh\u00ebn, mishrat e dh\u00ebmb\u00ebve ose mukoz\u00ebn orale. Buz\u00ebt preken m\u00eb s\u00eb shpeshti, ve\u00e7an\u00ebrisht pjesa e sip\u00ebrme (keilit granulomatoz). Edema orofaciale shpesh shoq\u00ebrohet me episode t\u00eb etheve dhe simptoma t\u00eb tjera. Kjo simptom\u00eb klinike zakonisht ndodh brenda disa or\u00ebsh me nj\u00eb tendenc\u00eb p\u00ebrs\u00ebrit\u00ebse brenda nj\u00eb kohe t\u00eb shkurt\u00ebr.<\/p>\n<p class=\"western\" lang=\"mk-MK\">Gjuha e \u00e7ar\u00eb<\/p>\n<p class=\"western\" lang=\"mk-MK\">Kjo simptom\u00eb e zakonshme karakterizohet nga nj\u00eb prerje gjat\u00ebsore n\u00eb mesin e gjuh\u00ebs dhe shfaqja e \u00e7arjeve t\u00ebrthore. Shoq\u00ebrohet me anomali gjenetike. Pacienti ndjen parestezie dhe humb ndjesin\u00eb p\u00ebr shije.<\/p>\n<p class=\"western\" lang=\"mk-MK\"><strong>Diagnoza:<\/strong><\/p>\n<p class=\"western\" lang=\"mk-MK\">Diagnostikimi i k\u00ebsaj s\u00ebmundjeje b\u00ebhet n\u00eb baz\u00eb t\u00eb dyshimit p\u00ebr treshen klasike simptomatike. Nuk ka nj\u00eb prov\u00eb laboratorike q\u00eb mund t\u00eb p\u00ebrcaktoj\u00eb pranin\u00eb e saj. Ekzaminimet histopatologjike p\u00ebrdoren shpesh n\u00eb analiz\u00ebn e edem\u00ebs.<\/p>\n<p class=\"western\" lang=\"mk-MK\"><strong>Trajtimi:<\/strong><\/p>\n<p class=\"western\" lang=\"mk-MK\">Nuk ka ndonj\u00eb trajtim specifik p\u00ebr SMR. Kortikosteroidet jan\u00eb nj\u00eb element thelb\u00ebsor n\u00eb trajtimin e k\u00ebsaj sindrome q\u00eb sigurojn\u00eb p\u00ebrmir\u00ebsim n\u00eb 50-80% t\u00eb pacient\u00ebve dhe ulin shanset e relapseve p\u00ebr 60-75%. Barnat anti-inflamatore jo-steroide, antihistaminik\u00ebt dhe antibiotik\u00ebt p\u00ebrfshihen gjithashtu n\u00eb trajtim. P\u00ebrdorimi i imunosupresant\u00ebve rekomandohet gjithashtu te disa pacient\u00eb. Trajtimi kirurgjik dhe rrezatimi rekomandohen p\u00ebr t\u00eb zvog\u00ebluar buz\u00ebt e fryra anormale.<\/p>\n\n<div style=\"font-size: 0px; height: 0px; line-height: 0px; margin: 0; padding: 0; clear: both;\"><\/div>","protected":false},"excerpt":{"rendered":"<p>Sindroma Melkersson-Rosenthal\/Melkersson-Rosenthal syndrome ICD: G 51.2 Prevalenca: e panjohur Sindroma Melkerson-Rosenthal \u00ebsht\u00eb nj\u00eb \u00e7rregullim i rrall\u00eb neurologjik i karakterizuar nga [&hellip;]<\/p>\n","protected":false},"author":22,"featured_media":165332,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_mo_disable_npp":"no","inline_featured_image":false},"categories":[3087],"tags":[56853],"imageURL":"https:\/\/sdk.mk\/wp-content\/uploads\/2022\/02\/04-Melkersson-Rosenthal-syndrome-1-650x366.png","thumbURL":"https:\/\/sdk.mk\/wp-content\/uploads\/2022\/02\/04-Melkersson-Rosenthal-syndrome-1-250x141.png","categoryNames":["Maqedonia"],"feature_caption":"","subtitle":"","views":"498","source":"\u0421\u043a\u043e\u043f\u0458\u0435, (\u0421\u0410\u041a\u0410\u041c\u0414\u0410\u041a\u0410\u0416\u0410\u041c.\u041c\u041a)","yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v15.0 - 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