{"id":165434,"date":"2022-02-06T09:38:54","date_gmt":"2022-02-06T08:38:54","guid":{"rendered":"https:\/\/sdk.mk\/?p=165434"},"modified":"2022-02-06T09:38:54","modified_gmt":"2022-02-06T08:38:54","slug":"ju-njoftojme-me-semundjet-e-rralla-sindroma-morvan","status":"publish","type":"post","link":"https:\/\/sdk.mk\/index.php\/maqedonia\/ju-njoftojme-me-semundjet-e-rralla-sindroma-morvan\/","title":{"rendered":"JU NJOFTOJM\u00cb ME S\u00cbMUNDJET E RRALLA: SINDROMA MORVAN"},"content":{"rendered":"<div class=\"f52428582a4b906b2d2e2a7d733c7d27\" data-index=\"7\" style=\"float: none; margin:10px 0 10px 0; text-align:center;\">\n<!-- MSP Ads Asynchronous JS Tag - Generated with Revive Adserver v5.4.1 -->\r\n<ins data-revive-zoneid=\"167\" data-revive-id=\"060fdb01f6430ec164d3519234aa4967\"><\/ins>\r\n<script async src=\"\/\/panel.ads.com.mk\/www\/delivery\/asyncjs.php\"><\/script>\n<\/div>\n<p class=\"western\" lang=\"mk-MK\"><em><strong>Sindroma Morvan\/Morvan\u2019s Syndrome<\/strong><\/em><\/p>\n<p class=\"western\" lang=\"mk-MK\">ICD: G 60.8<\/p>\n<p class=\"western\" lang=\"mk-MK\">Prevalenca: 1\/1.000.000<\/p>\n<p class=\"western\" lang=\"mk-MK\">Sindroma Morvan \u00ebsht\u00eb nj\u00eb s\u00ebmundje e fituar neurologjike, shum\u00eb e rrall\u00eb, potencialisht e rrezikshme p\u00ebr jet\u00ebn e karakterizuar nga aktiviteti i vazhduesh\u00ebm i fibrave muskulore, aktiviteti i d\u00ebmtuar i sistemit nervor autonom (i cili kontrollon funksionet e pavullnetshme trupore, t\u00eb tilla si funksioni i zemr\u00ebs, organet e tretjes, frym\u00ebmarrja, urinimi, ereksioni, etj) dhe \u00e7rregullimet e sistemit nervor qendror, kryesisht t\u00eb p\u00ebrfaq\u00ebsuara nga pagjum\u00ebsia e vazhdueshme. M\u00eb shpesh ndodh tek meshkujt n\u00eb mosh\u00eb t\u00eb vjet\u00ebr, megjith\u00ebse n\u00eb raste jasht\u00ebzakonisht t\u00eb rralla mund t\u00eb ndodh\u00eb edhe n\u00eb mosh\u00ebn f\u00ebmij\u00ebrore. N\u00eb disa raste, kjo simptom\u00eb mund t\u00eb shoq\u00ebrohet me nj\u00eb tumor t\u00eb timusit (nj\u00eb organ q\u00eb ekziston n\u00eb f\u00ebmij\u00ebrin\u00eb e hershme dhe m\u00eb pas zhduket spontanisht).<\/p>\n<p class=\"western\" lang=\"mk-MK\"><strong>Shkaqet:<\/strong><\/p>\n<p class=\"western\" lang=\"mk-MK\">Megjith\u00ebse nuk ka tregues t\u00eb besuesh;m q\u00eb do t\u00eb sqaronin shkakun e k\u00ebsaj gjendje, ekzistojn\u00eb disa supozime, t\u00eb tilla si: helmimi nga metalet e r\u00ebnda, funksioni i rritur dhe \u00e7rregullim i tiroides, disa tumore (si timoma) etj. Sidoqoft\u00eb, ka prova t\u00eb forta se thelbi i s\u00ebmundjes \u00ebsht\u00eb nj\u00eb reaksion autoimun, dmth trupi i njeriut prodhon antitrupa kund\u00ebr qelizave t\u00eb veta t\u00eb sh\u00ebndetshme, t\u00eb ashtuquajtura autoanititrupa. N\u00eb k\u00ebt\u00eb rast, k\u00ebto jan\u00eb autoantitrupa CASPR-2 dhe autoantitrupa LGI-1, t\u00eb cilat shkaktojn\u00eb mbindjeshm\u00ebri dhe stimulim t\u00eb tep\u00ebrt t\u00eb neuroneve, duke \u00e7uar n\u00eb p\u00ebrfshirje t\u00eb sistemit nervor qendror, periferik dhe autonom.<\/p>\n<p class=\"western\" lang=\"mk-MK\"><strong>Simptomat:<\/strong><\/p>\n<p class=\"western\" lang=\"mk-MK\">Kjo sindrom\u00eb p\u00ebrfshin nj\u00eb plejad\u00eb t\u00eb simptomave neurologjike q\u00eb p\u00ebrfshijn\u00eb sistemin nervor qendror, periferik dhe autonom. Shenjat nga sistemi nervor qendror jan\u00eb \u00e7rregullime n\u00eb t\u00eb gjykuar, pagjum\u00ebsi e r\u00ebnd\u00eb dhe e vazhdueshme, halucinacione, delirium, \u00e7orientim n\u00eb hap\u00ebsir\u00eb dhe koh\u00eb, humbje e kujtes\u00ebs.<\/p>\n<p class=\"western\" lang=\"mk-MK\">Nga sistemi nervor periferik dominon puna e pand\u00ebrprer\u00eb e fibrave muskulore, dhimbjet neuropatike, humbja e reflekseve t\u00eb ekstremiteteve. Simptomat nga sistemi nervor autonom jan\u00eb djersitje e tepruar, kruajtje, ethe, skuqje t\u00eb l\u00ebkur\u00ebs, kapsll\u00ebk, rrahje t\u00eb \u00e7rregullta t\u00eb zemr\u00ebs, takikardi, presion t\u00eb lart\u00eb t\u00eb gjakut.<\/p>\n<p class=\"western\" lang=\"mk-MK\">Simptomat e m\u00ebsip\u00ebrme jan\u00eb karakteristike p\u00ebr k\u00ebt\u00eb sindrom\u00eb, megjith\u00ebse ka pak t\u00eb ngjar\u00eb q\u00eb t\u00eb gjitha t\u00eb jen\u00eb t\u00eb pranishme te nj\u00eb pacient. Ndryshueshm\u00ebria n\u00eb pranin\u00eb e simptomave varet nga prania e autoantitrupave t\u00eb lartp\u00ebrmendur.<\/p>\n<p class=\"western\" lang=\"mk-MK\"><strong>Pasojat:<\/strong><\/p>\n<p class=\"western\" lang=\"mk-MK\">Megjith\u00ebse te disa pacient\u00eb simptomat t\u00ebrhiqen spontanisht pa pasoja, shumica kan\u00eb nevoj\u00eb p\u00ebr neurorehabilitim afatgjat\u00eb dhe trajtim t\u00eb zgjatur (me ila\u00e7e, fizioterapi). N\u00eb p\u00ebrgjith\u00ebsi, pasojat manifestohen nga sistemi nervor qendror, dmth mund t\u00eb ket\u00eb paq\u00ebndrueshm\u00ebri n\u00eb ecje (ecja me k\u00ebmb\u00eb t\u00eb hapura), pastaj probleme t\u00eb kujtes\u00ebs dhe t\u00eb funksioneve tjera kognitive (t\u00eb m\u00ebsuarit, leximi). Sidoqoft\u00eb, prognoza varet nga rrjedha klinike e s\u00ebmundjes dhe shkalla e p\u00ebrfshirjes t\u00eb strukturave t\u00eb sistemit nervor qendror, periferik dhe autonom, por kur b\u00ebhet fjal\u00eb p\u00ebr sulme ose konvulsione, ato jan\u00eb t\u00eb rralla.<\/p>\n<p class=\"western\" lang=\"mk-MK\"><strong>Diagnoza dhe trajtimi:<\/strong><\/p>\n<p class=\"western\" lang=\"mk-MK\">Diagnostikimi b\u00ebhet n\u00eb baz\u00eb t\u00eb rrjedh\u00ebs klinike dhe pranis\u00eb s\u00eb antitrupave n\u00eb gjak ose n\u00eb l\u00ebngun cerebrospinal. P\u00ebr m\u00eb tep\u00ebr, mund t\u00eb b\u00ebhen teste t\u00eb tjera, t\u00eb tilla si tomografia e kompjuterizuar ose rezonanca magnetike, por n\u00eb shumic\u00ebn e rasteve, k\u00ebto incizime jan\u00eb pa ndryshime.<\/p>\n<p class=\"western\" lang=\"mk-MK\">Trajtimi i s\u00ebmundjes b\u00ebhet me terapi medikamentoze &#8211; kortikosteroide q\u00eb ndikon n\u00eb zvog\u00eblimin e p\u00ebrgjigjes imune dhe p\u00ebrmes plazmaferez\u00ebs.<\/p>\n\n<div style=\"font-size: 0px; height: 0px; line-height: 0px; margin: 0; padding: 0; clear: both;\"><\/div>","protected":false},"excerpt":{"rendered":"<p>Sindroma Morvan\/Morvan\u2019s Syndrome ICD: G 60.8 Prevalenca: 1\/1.000.000 Sindroma Morvan \u00ebsht\u00eb nj\u00eb s\u00ebmundje e fituar neurologjike, shum\u00eb e rrall\u00eb, potencialisht [&hellip;]<\/p>\n","protected":false},"author":22,"featured_media":165435,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_mo_disable_npp":"no","inline_featured_image":false},"categories":[3087],"tags":[56891],"imageURL":"https:\/\/sdk.mk\/wp-content\/uploads\/2022\/02\/06-Morvans-Syndrome-1-650x366.png","thumbURL":"https:\/\/sdk.mk\/wp-content\/uploads\/2022\/02\/06-Morvans-Syndrome-1-250x141.png","categoryNames":["Maqedonia"],"feature_caption":"","subtitle":"","views":"112","source":"\u0421\u043a\u043e\u043f\u0458\u0435, (\u0421\u0410\u041a\u0410\u041c\u0414\u0410\u041a\u0410\u0416\u0410\u041c.\u041c\u041a)","yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v15.0 - 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