{"id":165961,"date":"2022-02-14T09:10:52","date_gmt":"2022-02-14T08:10:52","guid":{"rendered":"https:\/\/sdk.mk\/?p=165961"},"modified":"2022-02-14T09:10:52","modified_gmt":"2022-02-14T08:10:52","slug":"ju-njoftojme-me-semundjet-e-rralla-miastenia-gravis","status":"publish","type":"post","link":"https:\/\/sdk.mk\/index.php\/maqedonia\/ju-njoftojme-me-semundjet-e-rralla-miastenia-gravis\/","title":{"rendered":"JU NJOFTOJM\u00cb ME S\u00cbMUNDJET E RRALLA: MIASTENIA GRAVIS"},"content":{"rendered":"<div class=\"f52428582a4b906b2d2e2a7d733c7d27\" data-index=\"7\" style=\"float: none; margin:10px 0 10px 0; text-align:center;\">\n<!-- MSP Ads Asynchronous JS Tag - Generated with Revive Adserver v5.4.1 -->\r\n<ins data-revive-zoneid=\"167\" data-revive-id=\"060fdb01f6430ec164d3519234aa4967\"><\/ins>\r\n<script async src=\"\/\/panel.ads.com.mk\/www\/delivery\/asyncjs.php\"><\/script>\n<\/div>\n<p class=\"western\" lang=\"mk-MK\"><em><strong>Miastenia gravis\/Myasthenia gravis<\/strong><\/em><\/p>\n<p class=\"western\" lang=\"mk-MK\">ICD: G 70.01<\/p>\n<p class=\"western\" lang=\"mk-MK\">Prevalenca: 1-9\/100.000<\/p>\n<p class=\"western\" lang=\"mk-MK\">Miastenia gravis \u00ebsht\u00eb nj\u00eb s\u00ebmundje e nj\u00eb natyre autoimune me dob\u00ebsi progresive t\u00eb muskujve si rezultat i \u00e7rregullimeve n\u00eb lidhjet neuromuskulare. Muskujt e syve, muskujt p\u00ebrtyp\u00ebs dhe muskujt e fytyr\u00ebs preken zakonisht, dhe m\u00eb rrall\u00eb muskujt e p\u00ebrfshir\u00eb n\u00eb funksionin e frym\u00ebmarrjes. Sipas statistikave, miastenia gravis haset m\u00eb shpesh tek grat\u00eb e moshuara, megjith\u00ebse s\u00ebmundja \u00ebsht\u00eb raportuar koh\u00ebt e fundit edhe n\u00eb brezin e ri.<\/p>\n<p class=\"western\" lang=\"mk-MK\">Emri i s\u00ebmundjes vjen nga fjala latine \u201emyasthenia\u201c, q\u00eb do t\u00eb thot\u00eb dob\u00ebsi e muskujve, dhe fjala \u201egravis\u201c, q\u00eb do t\u00eb thot\u00eb serioze, e v\u00ebshtir\u00eb. P\u00ebrshkrimi i par\u00eb i pacient\u00ebve me miastenia gravis u dha n\u00eb 1672 nga Thomas Willis (1621-1675), nj\u00eb mjek anglez i njohur p\u00ebr k\u00ebrkimet e tij mbi sistemin nervor.<\/p>\n<p class=\"western\" lang=\"mk-MK\"><strong>Shkaqet e s\u00ebmundjes:<\/strong><\/p>\n<p class=\"western\" lang=\"mk-MK\">Arsyeja kryesore p\u00ebr zhvillimin e s\u00ebmundjes mbetet ende e panjohur. \u00c7rregullimet i referohen zon\u00ebs s\u00eb lidhjes neuromuskulare, dometh\u00ebn\u00eb pjes\u00ebs ku ndodhen receptor\u00ebt p\u00ebr neurotransmetuesin acetilkolin\u00eb. N\u00eb zon\u00ebn e sinaps\u00ebs neuromuskulare, ndodh bllokada e receptor\u00ebve t\u00eb acetilkolin\u00ebs, e cila parandalon krijimin e potencialit t\u00eb veprimit muskulor dhe transmetimin e impulseve nervore n\u00eb muskul. Bllokimi ndodh p\u00ebr shkak t\u00eb pranis\u00eb s\u00eb antitrupave ndaj receptor\u00ebt e acetilkolin\u00ebs. Miastenia gravis mund t\u00eb jet\u00eb e lindur ose e fituar.<\/p>\n<p class=\"western\" lang=\"mk-MK\">Forma e par\u00eb \u00ebsht\u00eb shum\u00eb m\u00eb e rrall\u00eb dhe shkaktohet nga mutacionet e gjeneve. Forma e fituar e s\u00ebmundjes mund t\u00eb shfaqet si pjes\u00eb e timomegalis\u00eb (hiperplazis\u00eb beninje t\u00eb timusit) ose si pjes\u00eb e tumoreve. M\u00eb rrall\u00eb, shkaku i s\u00ebmundjes mund t\u00eb jet\u00eb me origjin\u00eb autoimune (skleroderma ose dermatomioziti).<\/p>\n<p class=\"western\" lang=\"mk-MK\">Ka shum\u00eb raste kur miastenia gravis zhvillohet s\u00eb bashku me nj\u00eb lloj t\u00eb caktuar t\u00eb tumorit. Kjo \u00ebsht\u00eb haset te tumoret e organeve gjenitale (prostat\u00ebs, vezoreve), m\u00eb rrall\u00eb t\u00eb m\u00ebl\u00e7is\u00eb dhe mushk\u00ebrive.<\/p>\n<p class=\"western\" lang=\"mk-MK\"><strong>Simptomat e s\u00ebmundjes:<\/strong><\/p>\n<p class=\"western\" lang=\"mk-MK\">Simptomat mund t\u00eb ndryshojn\u00eb ose t\u00eb shfaqen t\u00eb kombinuara n\u00eb var\u00ebsi t\u00eb form\u00ebs s\u00eb s\u00ebmundjes dhe faz\u00ebs s\u00eb saj. Forma okulare e miastenia gravis prek muskujt e syve.<\/p>\n<p class=\"western\" lang=\"mk-MK\">Pasojat e k\u00ebsaj forme t\u00eb s\u00ebmundjes mund t\u00eb jen\u00eb: v\u00ebshtir\u00ebsi n\u00eb fokusimin e shikimit; strabiz\u00ebm; vizion i dyfisht\u00eb; paaft\u00ebsi p\u00ebr t\u00eb par\u00eb objekte t\u00eb larg\u00ebta ose shum\u00eb t\u00eb af\u00ebrta p\u00ebr nj\u00eb periudh\u00eb t\u00eb zgjatur kohe; r\u00ebnie t\u00eb qepall\u00ebs s\u00eb sip\u00ebrme (ptoz\u00eb).<\/p>\n<p class=\"western\" lang=\"mk-MK\">Miastenia gravis prek gjithashtu z\u00ebrin dhe t\u00eb folurit, andaj pacient\u00ebt ballafaqohen me: nryshim\u00eb t\u00eb z\u00ebrit, z\u00ebri fiton nj\u00eb ton t\u00eb but\u00eb dhe hundor; v\u00ebshtir\u00ebsi n\u00eb t\u00eb folur (pacienti lodhet edhe pas disa minutash bised\u00eb); v\u00ebshtir\u00ebsi n\u00eb t\u00eb ngr\u00ebn\u00eb (pacienti ka v\u00ebshtir\u00ebsi n\u00eb p\u00ebrtypjen e ushqimit t\u00eb ngurt\u00eb p\u00ebr shkak t\u00eb dob\u00ebsis\u00eb s\u00eb muskujve p\u00ebrkat\u00ebs).<\/p>\n<p class=\"western\" lang=\"mk-MK\">Forma muskuloskeletale e s\u00ebmundjes shoq\u00ebrohet me nj\u00eb lodhje t\u00eb shprehur n\u00eb nj\u00eb ose nj\u00eb pjes\u00eb tjet\u00ebr t\u00eb trupit. N\u00eb shumic\u00ebn e rasteve, kjo vlen p\u00ebr gjymtyr\u00ebt. M\u00eb e rrezikshmja \u00ebsht\u00eb forma e gjeneralizuar e s\u00ebmundjes. Manifestohet me dob\u00ebsi t\u00eb muskujve t\u00eb frym\u00ebmarrjes e cila mund t\u00eb \u00e7oj\u00eb n\u00eb zhvillimin e hipoksis\u00eb akute dhe vdekjes.<\/p>\n<p class=\"western\" lang=\"mk-MK\"><strong>Diagnostikimi:<\/strong><\/p>\n<p class=\"western\"><span lang=\"mk-MK\">Miastenia gravis \u00ebsht\u00eb nj\u00eb s\u00ebmundje mjaft e rrall\u00eb. Diagnostikimi b\u00ebhet p\u00ebrmes: historis\u00eb klinike; ekzaminimit fizik; testit me prostigmin\u00eb; testit me <\/span><span lang=\"en-US\">edrofonium; elektromiografis\u00eb<\/span><span lang=\"mk-MK\">; p\u00ebrcaktimi i antitrupthave ndaj receptor\u00ebve t\u00eb acetilkolin\u00ebs n\u00eb gjak; ekzamini okulistik; tomografia kompjuterike e krah\u00ebrorit; rezonanca magnetike; testi i funksionit t\u00eb mushk\u00ebrive.<\/span><\/p>\n<p class=\"western\" lang=\"mk-MK\">Gjat\u00eb ekzaminimeve, \u00ebsht\u00eb e r\u00ebnd\u00ebsishme t\u00eb p\u00ebrjashtohen t\u00eb gjitha s\u00ebmundjet e mundshme, simptomat e t\u00eb cilave jan\u00eb deri diku t\u00eb ngjashme me manifestimet e miastenia gravis. K\u00ebtu p\u00ebrfshihen s\u00ebmundje inflamatore (meningjit, encefalit), tumore t\u00eb trungut t\u00eb trurit (hemangioblastoma, glioma), s\u00ebmundje neuromuskulare (miopati, skleroza amiotrofike laterale), \u00e7rregullime cerebrovaskulare.<\/p>\n<p class=\"western\" lang=\"mk-MK\"><strong>Trajtimi:<\/strong><\/p>\n<p class=\"western\" lang=\"mk-MK\">N\u00eb var\u00ebsi t\u00eb simptomave dhe faz\u00ebs s\u00eb zhvillimit t\u00eb s\u00ebmundjes, lloji i terapis\u00eb s\u00eb k\u00ebrkuar mund t\u00eb ndryshoj\u00eb. Nga terapia farmakologjike aplikohen t\u00eb ashtuquajturat antikolinergjik\u00eb q\u00eb parandalojn\u00eb shp\u00ebrb\u00ebrjen e acetilkolin\u00ebs. Ky grup p\u00ebrfshin ila\u00e7in Prostigmine (Neostigmine). P\u00ebrparimi i s\u00ebmundjes p\u00ebrfshin masa terapeutike m\u00eb agresive. P\u00ebrfitimet nga p\u00ebrdorimi i tyre jan\u00eb shum\u00eb m\u00eb dometh\u00ebn\u00ebse sesa efektet an\u00ebsore t\u00eb mundshme, ve\u00e7an\u00ebrisht kur b\u00ebhet fjal\u00eb p\u00ebr ruajtjen jo vet\u00ebm t\u00eb sh\u00ebndetit, por edhe t\u00eb jet\u00ebs.<\/p>\n<p class=\"western\" lang=\"mk-MK\">K\u00ebto p\u00ebrfshijn\u00eb procedurat e m\u00ebposhtme q\u00eb duhet t\u00eb ceken: ventilimi mekanik kur frym\u00ebmarrja spontane \u00ebsht\u00eb e pamundur; plazmafereza; terapia profesionale dhe fizioterapia &#8211; k\u00ebto dy procedura do t\u00eb ndihmojn\u00eb pacientin t\u00eb merret me luhatjet e forc\u00ebs s\u00eb muskujve. P\u00ebrve\u00e7 k\u00ebsaj, heqja kirurgjikale e gj\u00ebndr\u00ebs s\u00eb timusit mund t\u00eb jet\u00eb e nevojshme.<\/p>\n\n<div style=\"font-size: 0px; height: 0px; line-height: 0px; margin: 0; padding: 0; clear: both;\"><\/div>","protected":false},"excerpt":{"rendered":"<p>Miastenia gravis\/Myasthenia gravis ICD: G 70.01 Prevalenca: 1-9\/100.000 Miastenia gravis \u00ebsht\u00eb nj\u00eb s\u00ebmundje e nj\u00eb natyre autoimune me dob\u00ebsi progresive [&hellip;]<\/p>\n","protected":false},"author":22,"featured_media":165962,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_mo_disable_npp":"no","inline_featured_image":false},"categories":[3087],"tags":[57027],"imageURL":"https:\/\/sdk.mk\/wp-content\/uploads\/2022\/02\/14-Myasthenia-gravis-1-650x366.png","thumbURL":"https:\/\/sdk.mk\/wp-content\/uploads\/2022\/02\/14-Myasthenia-gravis-1-250x141.png","categoryNames":["Maqedonia"],"feature_caption":"","subtitle":"","views":"4599","source":"\u0421\u043a\u043e\u043f\u0458\u0435, (\u0421\u0410\u041a\u0410\u041c\u0414\u0410\u041a\u0410\u0416\u0410\u041c.\u041c\u041a)","yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v15.0 - 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