{"id":166031,"date":"2022-02-15T09:00:09","date_gmt":"2022-02-15T08:00:09","guid":{"rendered":"https:\/\/sdk.mk\/?p=166031"},"modified":"2022-02-15T09:00:09","modified_gmt":"2022-02-15T08:00:09","slug":"ju-njoftojme-me-semundjet-e-rralla-sindroma-barter","status":"publish","type":"post","link":"https:\/\/sdk.mk\/index.php\/maqedonia\/ju-njoftojme-me-semundjet-e-rralla-sindroma-barter\/","title":{"rendered":"JU NJOFTOJM\u00cb ME S\u00cbMUNDJET E RRALLA: SINDROMA BARTER"},"content":{"rendered":"<div class=\"f52428582a4b906b2d2e2a7d733c7d27\" data-index=\"7\" style=\"float: none; margin:10px 0 10px 0; text-align:center;\">\n<!-- MSP Ads Asynchronous JS Tag - Generated with Revive Adserver v5.4.1 -->\r\n<ins data-revive-zoneid=\"167\" data-revive-id=\"060fdb01f6430ec164d3519234aa4967\"><\/ins>\r\n<script async src=\"\/\/panel.ads.com.mk\/www\/delivery\/asyncjs.php\"><\/script>\n<\/div>\n<p><em><strong>Sindroma Barter\/Bartter syndrome<\/strong><\/em><\/p>\n<p>ICD &#8211; 10: E 26.8<\/p>\n<p>Prevalenca: e panjohur<\/p>\n<p>Sindroma Barter \u00ebsht\u00eb nj\u00eb \u00e7rregullim n\u00eb t\u00eb cilin veshkat sekretojn\u00eb sasi t\u00eb tep\u00ebrt t\u00eb elektroliteve (kalium, klorur natriumi) q\u00eb \u00e7on n\u00eb nivele t\u00eb ul\u00ebta t\u00eb kaliumit n\u00eb gjak (hipokalemi) dhe nivele t\u00eb larta t\u00eb hormoneve aldosteron dhe renin\u00eb. Sindroma Barter zakonisht trash\u00ebgohet dhe shkaktohet nga nj\u00eb gjen recesiv, k\u00ebshtu q\u00eb nj\u00eb person duhet t\u00eb trash\u00ebgoj\u00eb dy gjene recesive p\u00ebr t\u00eb shfaqur sindrom\u00ebn, nj\u00eb nga secili prind. Gjendja \u00ebsht\u00eb em\u00ebruar pas endokrinologut amerikan Dr. Frederic Barter, i cili, s\u00eb bashku me Dr. Pacita Pronove, e p\u00ebrshkruan s\u00ebmundjen p\u00ebr her\u00eb t\u00eb par\u00eb n\u00eb 1960.<\/p>\n<p>Sindroma Barter \u00ebsht\u00eb nj\u00eb s\u00ebmundje e trash\u00ebguar e veshkave q\u00eb mendohet se shkaktohet nga pamund\u00ebsia e veshkave p\u00ebr t\u00eb riabsorbuar kaliumin. Si rezultat, veshkat largojn\u00eb shum\u00eb kalium nga trupi. Sindroma Barter trash\u00ebgohet n\u00eb nj\u00eb form\u00eb autosomale recesive, edhe pse ndonj\u00ebher\u00eb mund t\u00eb shfaqet te dikush pa nj\u00eb histori familjare. Nuk dihet sakt\u00ebsisht sa shpesh haset, por nj\u00eb studim vler\u00ebson se prevalenca \u00ebsht\u00eb 1 deri n\u00eb 2 raste p\u00ebr milion njer\u00ebz.<\/p>\n<p><strong>Simptomat:<\/strong><\/p>\n<p>F\u00ebmij\u00ebt me sindrom\u00ebn Barter rriten ngadal\u00eb dhe duken t\u00eb kequshqyer. Ata mund t\u00eb ken\u00eb dob\u00ebsi t\u00eb muskujve dhe etje t\u00eb tepruar, mund t\u00eb prodhojn\u00eb sasi t\u00eb m\u00ebdha t\u00eb urin\u00ebs dhe mund t\u00eb zhvillojn\u00eb ngecje mendore. Niveli i klorurit t\u00eb natriumit dhe ujit n\u00eb gjak zvog\u00eblohet. Trupi p\u00ebrpiqet ta kompensoj\u00eb k\u00ebt\u00eb duke prodhuar m\u00eb shum\u00eb aldosteron dhe renin\u00eb &#8211; k\u00ebto hormone ulin nivelin e kaliumit n\u00eb gjak.<\/p>\n<p>Sindroma Barter karakterizohet nga hipokalemia q\u00eb vjen nga humbja e kaliumit n\u00eb veshka, rritja e aktivitetit t\u00eb renin\u00ebs dhe aldosteronit n\u00eb gjak, por me presion normal arterial. \u00c7rregullimi kryesor te kjo sindrom\u00eb \u00ebsht\u00eb l\u00ebvizja e gabuar e elektroliteve brenda tubuleve renale. P\u00ebrve\u00e7 uljes s\u00eb nivelit t\u00eb kaliumit n\u00eb gjak, manifestohet edhe ulje e nivelit t\u00eb magnezit n\u00eb gjak (hipomagnezemi) gjithashtu si rezultat i sekretimit t\u00eb rritur t\u00eb magnezit n\u00eb urin\u00eb.<br \/>\nSimptomat e sindrom\u00ebs Barter p\u00ebrfshijn\u00eb: lodhje dhe dob\u00ebsi e p\u00ebrgjithshme; rritje t\u00eb urinimit (poliuri); etje e shtuar (polidipsi); zgjim nat\u00ebn p\u00ebr t\u00eb urinuar (nokturi); dehidratim i leht\u00eb; d\u00ebshir\u00eb p\u00ebr krip\u00eb; ng\u00ebr\u00e7e t\u00eb muskujv\u0435; kapsll\u00ebk.<br \/>\nShkalla e rritjes s\u00eb f\u00ebmij\u00ebve me k\u00ebt\u00eb \u00e7rregullim mund t\u00eb jet\u00eb n\u00ebn at\u00eb q\u00eb do t\u00eb pritej bazuar n\u00eb mosh\u00ebn dhe gjinin\u00eb e tyre (rritje e ngadalt\u00eb). N\u00ebse nuk trajtohen, f\u00ebmij\u00ebt mund t\u00eb mbeten shum\u00eb m\u00eb t\u00eb shkurt\u00ebr.<\/p>\n<p>Disa persona q\u00eb kan\u00eb \u00e7ekuilib\u00ebr t\u00eb r\u00ebnd\u00ebsish\u00ebm t\u00eb elektroliteve mund t\u00eb zhvillojn\u00eb komplikime t\u00eb r\u00ebnda, t\u00eb tilla si rrahje t\u00eb parregullta t\u00eb zemr\u00ebs ose dob\u00ebsi t\u00eb muskujve. Edhe pse t\u00eb rralla, n\u00ebse nuk trajtohen, k\u00ebto aritmi kardiake mund t\u00eb p\u00ebrparojn\u00eb potencialisht dhe t\u00eb shkaktojn\u00eb arrest kardiak dhe vdekje t\u00eb papritur. Nivelet e larta t\u00eb kalciumit n\u00eb urin\u00eb mund t\u00eb \u00e7ojn\u00eb n\u00eb depozitimin e kalciumit n\u00eb veshka (nefrokalcinoz\u00eb), formimin e gur\u00ebve n\u00eb veshka dhe p\u00ebrfundimisht t\u00eb ndikojn\u00eb n\u00eb funksionimin e veshkave.<\/p>\n<p><strong>Diagnoza:<\/strong><\/p>\n<p>Testet laboratorike q\u00eb tregojn\u00eb nivele jonormale t\u00eb kaliumit dhe hormoneve n\u00eb gjak konfirmojn\u00eb diagnoz\u00ebn. Diagnoza p\u00ebrfundimtare b\u00ebhet n\u00eb baz\u00eb t\u00eb testeve laboratorike t\u00eb kaliumit, magnezit, renin\u00ebs, angiotensin\u00ebs, aldosteronit dhe prostaglandin\u00ebs E2: nivele t\u00eb ul\u00ebta t\u00eb kaliumit n\u00eb gjak; nivele t\u00eb larta t\u00eb kaliumit n\u00eb urin\u00eb; nivele t\u00eb ul\u00ebta t\u00eb klorurit n\u00eb gjak; nivele t\u00eb larta t\u00eb klorurit n\u00eb urin\u00eb; nivele t\u00eb larta t\u00eb hormoneve renin\u00eb dhe aldosteron n\u00eb gjak.<\/p>\n<p><strong>Trajtimi:<\/strong><\/p>\n<p>Trajtimi i sindrom\u00ebs Barter fokusohet n\u00eb mbajtjen e kaliumit n\u00eb nj\u00eb nivel normal. Kjo arrihet duke konsumuar ushqim t\u00eb pasur me kalium dhe duke marr\u00eb shtesa kaliumi n\u00ebse \u00ebsht\u00eb e nevojshme.<br \/>\nEkzistojn\u00eb gjithashtu ila\u00e7e q\u00eb zvog\u00eblojn\u00eb eliminimin e kaliumit n\u00eb urin\u00eb, t\u00eb tilla si spironolactone, triamterene ose amiloride. Ila\u00e7et e tjera t\u00eb p\u00ebrdorura p\u00ebr t\u00eb trajtuar sindrom\u00ebn Barter mund t\u00eb p\u00ebrfshijn\u00eb indometacin\u00ebn, captoprilin dhe tek f\u00ebmij\u00ebt, hormonin e rritjes.<\/p>\n\n<div style=\"font-size: 0px; height: 0px; line-height: 0px; margin: 0; padding: 0; clear: both;\"><\/div>","protected":false},"excerpt":{"rendered":"<p>Sindroma Barter\/Bartter syndrome ICD &#8211; 10: E 26.8 Prevalenca: e panjohur Sindroma Barter \u00ebsht\u00eb nj\u00eb \u00e7rregullim n\u00eb t\u00eb cilin veshkat [&hellip;]<\/p>\n","protected":false},"author":22,"featured_media":166032,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_mo_disable_npp":"no","inline_featured_image":false},"categories":[3087],"tags":[],"imageURL":"https:\/\/sdk.mk\/wp-content\/uploads\/2022\/02\/15-Bartter-syndrome-1-650x366.png","thumbURL":"https:\/\/sdk.mk\/wp-content\/uploads\/2022\/02\/15-Bartter-syndrome-1-250x141.png","categoryNames":["Maqedonia"],"feature_caption":"","subtitle":"","views":"233","source":"\u0421\u043a\u043e\u043f\u0458\u0435, (\u0421\u0410\u041a\u0410\u041c\u0414\u0410\u041a\u0410\u0416\u0410\u041c.\u041c\u041a)","yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v15.0 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>JU NJOFTOJM\u00cb ME S\u00cbMUNDJET E RRALLA: SINDROMA BARTER - \u0421\u0430\u043a\u0430\u043c \u0414\u0430 \u041a\u0430\u0436\u0430\u043c<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/sdk.mk\/index.php\/maqedonia\/ju-njoftojme-me-semundjet-e-rralla-sindroma-barter\/\" \/>\n<meta property=\"og:locale\" content=\"mk_MK\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"JU NJOFTOJM\u00cb ME S\u00cbMUNDJET E RRALLA: SINDROMA BARTER - \u0421\u0430\u043a\u0430\u043c \u0414\u0430 \u041a\u0430\u0436\u0430\u043c\" \/>\n<meta property=\"og:description\" content=\"Sindroma Barter\/Bartter syndrome ICD &#8211; 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