{"id":187823,"date":"2023-02-03T08:30:48","date_gmt":"2023-02-03T07:30:48","guid":{"rendered":"https:\/\/sdk.mk\/?p=187823"},"modified":"2023-02-03T08:30:48","modified_gmt":"2023-02-03T07:30:48","slug":"ju-njoftojme-me-semundjet-e-rralla-sindroma-pfapa","status":"publish","type":"post","link":"https:\/\/sdk.mk\/index.php\/maqedonia\/ju-njoftojme-me-semundjet-e-rralla-sindroma-pfapa\/","title":{"rendered":"JU NJOFTOJM\u00cb ME S\u00cbMUNDJET E RRALLA: SINDROMA PFAPA"},"content":{"rendered":"<div class=\"f52428582a4b906b2d2e2a7d733c7d27\" data-index=\"7\" style=\"float: none; margin:10px 0 10px 0; text-align:center;\">\n<!-- MSP Ads Asynchronous JS Tag - Generated with Revive Adserver v5.4.1 -->\r\n<ins data-revive-zoneid=\"167\" data-revive-id=\"060fdb01f6430ec164d3519234aa4967\"><\/ins>\r\n<script async src=\"\/\/panel.ads.com.mk\/www\/delivery\/asyncjs.php\"><\/script>\n<\/div>\n<p lang=\"mk-MK\"><em><strong><span style=\"font-size: medium;\">Sindroma e etheve periodike, stomatit aftoz, faringjit dhe adenit cervikal\/PFAPA Syndrome<\/span><\/strong><\/em><\/p>\n<p lang=\"mk-MK\"><span style=\"font-size: medium;\">ICD E 85.0<\/span><\/p>\n<p lang=\"mk-MK\"><span style=\"font-size: medium;\">Prevalenca: e panjohur<\/span><\/p>\n<p lang=\"mk-MK\"><span style=\"font-size: medium;\">Ethet periodike, stomatiti aftoz, faringjiti dhe adeniti cervikal (\u00ebnjtje e nyjeve limfatike t\u00eb qaf\u00ebs), ose shkurt sindroma PFAPA, \u00ebsht\u00eb nj\u00eb s\u00ebmundje me ecuri periodike q\u00eb i p\u00ebrket grupit heterogjen t\u00eb s\u00ebmundjeve dhe karakterizohet nga episode t\u00eb shkurtra t\u00eb gjendjes akute q\u00eb p\u00ebrs\u00ebriten rregullisht gjat\u00eb disa viteve t\u00eb shoq\u00ebruara me periudha normale t\u00eb sh\u00ebndetshme nd\u00ebrmjet atyre episodeve.<\/span><\/p>\n<p lang=\"mk-MK\"><span style=\"font-size: medium;\">Kjo sindrom\u00eb u p\u00ebrshkrua dhe u v\u00ebzhgua p\u00ebr her\u00eb t\u00eb par\u00eb nga Dr. Gary Marshall n\u00eb 1987 n\u00eb 12 f\u00ebmij\u00eb nga Tenesi dhe Alabama. N\u00eb literatur\u00eb mund t\u00eb gjendet edhe me emrin \u201cSindroma Marshall\u201d &#8211; em\u00ebr i dh\u00ebn\u00eb pas nj\u00eb an\u00ebtari t\u00eb s\u00ebmur\u00eb t\u00eb nj\u00eb familjeje. M\u00eb shum\u00eb se 700 raste jan\u00eb raportuar nga kontinente dhe raca t\u00eb ndryshme. Nuk ka dyshim se shumica e rasteve nuk raportohen ose nuk diagnostikohen. Kjo sindrom\u00eb \u00ebsht\u00eb sindroma m\u00eb e zakonshme e etheve periodike tek f\u00ebmij\u00ebt.<\/span><\/p>\n<p lang=\"mk-MK\"><strong><span style=\"font-size: medium;\">Shkaqet:<\/span><\/strong><\/p>\n<p lang=\"mk-MK\"><span style=\"font-size: medium;\">Nuk dihet ende shkaku i k\u00ebsaj s\u00ebmundjeje, megjith\u00ebse \u00ebsht\u00eb v\u00ebrtetuar se p\u00ebrfshihen procese inflamatore, por nuk \u00ebsht\u00eb plot\u00ebsisht e qart\u00eb pse zhvillohet episodi akut. S\u00ebmundja nuk \u00ebsht\u00eb ngjit\u00ebse dhe nuk transmetohet mes njer\u00ebzve. Infeksionet mund t\u00eb jen\u00eb nxitje p\u00ebr p\u00ebrs\u00ebritjen e episodeve. Jan\u00eb p\u00ebrshkruar raste t\u00eb s\u00ebmundjes n\u00eb nj\u00eb familje, por deri m\u00eb sot nuk \u00ebsht\u00eb identifikuar asnj\u00eb faktor gjenetik p\u00ebrgjegj\u00ebs p\u00ebr vet\u00eb s\u00ebmundjen.<\/span><\/p>\n<p lang=\"mk-MK\"><strong><span style=\"font-size: medium;\">Simptomat:<\/span><\/strong><\/p>\n<p lang=\"mk-MK\"><span style=\"font-size: medium;\">Zakonisht kjo sindrom\u00eb shfaqet tek f\u00ebmij\u00ebt n\u00ebn 5 vje\u00e7 dhe m\u00eb rrall\u00eb tek t\u00eb rriturit. Simptomat p\u00ebrfshijn\u00eb temperatur\u00eb t\u00eb lart\u00eb q\u00eb zgjat nga tre deri n\u00eb gjasht\u00eb dit\u00eb dhe p\u00ebrs\u00ebritet \u00e7do 21-28 dit\u00eb e shoq\u00ebruar me dhimbje trupi, lodhje, afte n\u00eb goj\u00eb, faringjit dhe adenit cervikal. Artralgjia (dhimbja e ky\u00e7eve), encefaliti dhe problemet e sjelljes shfaqen m\u00eb rrall\u00eb. Gjat\u00eb episodit akut nuk mund t\u00eb v\u00ebrtetohet prania e infeksionit. Faktor\u00ebt inflamator\u00eb (leukocitet, sedimentimi, CRP-ja) rriten gjat\u00eb koh\u00ebzgjatjes s\u00eb simptomave dhe jan\u00eb normale gjat\u00eb pushimeve. P\u00ebr shkak t\u00eb temperatur\u00ebs jasht\u00ebzakonisht t\u00eb lart\u00eb dhe gjendjes s\u00eb p\u00ebrgjithshme jo t\u00eb mir\u00eb, f\u00ebmij\u00ebve shpesh u rekomandohen antibiotik\u00eb, por s\u00ebmundja nuk p\u00ebrmir\u00ebsohet me aplikimin e tyre. Tek f\u00ebmij\u00ebt, simptomat largohen pas disa vitesh, por tek t\u00eb rriturit ato vazhdojn\u00eb p\u00ebr nj\u00eb koh\u00eb m\u00eb t\u00eb gjat\u00eb. Simptomat ndryshojn\u00eb nga personi n\u00eb person dhe jo gjithmon\u00eb jan\u00eb t\u00eb pranishme t\u00eb gjitha simptomat e s\u00ebmundjes. Duke qen\u00eb se nuk ka teste apo procedura t\u00eb ve\u00e7anta diagnostikuese p\u00ebr ta v\u00ebrtetuar at\u00eb, diagnoza vendoset n\u00eb baz\u00eb t\u00eb pasqyr\u00ebs klinike. Gjegj\u00ebsisht, pasqyra klinike p\u00ebrfshin tre ose m\u00eb shum\u00eb episode t\u00eb etheve q\u00eb zgjasin m\u00eb shum\u00eb se pes\u00eb dit\u00eb dhe p\u00ebrs\u00ebriten n\u00eb intervale, pa ndonj\u00eb shkak akut n\u00eb sfond. Ajo shoq\u00ebrohet me stomatit aftoz, faringjit, adenit cervikal. Analiza e gjakut tregon leukocitoz\u00eb dhe rritje t\u00eb sedimentimit dhe CRP n\u00eb faz\u00ebn akute, dhe midis sulmeve febrile vlerat jan\u00eb normale.<\/span><\/p>\n<p lang=\"mk-MK\"><strong><span style=\"font-size: medium;\">Pasojat:<\/span><\/strong><\/p>\n<p lang=\"mk-MK\"><span style=\"font-size: medium;\">N\u00ebse ecuria akute e s\u00ebmundjes trajtohet n\u00eb m\u00ebnyr\u00eb t\u00eb duhur, s\u00ebmundja nuk l\u00eb pasoja, normalisht, varet nga gjendja e p\u00ebrgjithshme e pacientit dhe n\u00ebse ka s\u00ebmundje t\u00eb tjera shoq\u00ebruese.<\/span><\/p>\n<p lang=\"mk-MK\"><strong><span style=\"font-size: medium;\">Trajtimi:<\/span><\/strong><\/p>\n<p lang=\"mk-MK\"><span style=\"font-size: medium;\">Nuk ka trajtim specifik p\u00ebr k\u00ebt\u00eb sindrom\u00eb. Q\u00ebllimi i trajtimit \u00ebsht\u00eb kontrolli i simptomave gjat\u00eb episodit t\u00eb s\u00ebmundjes. N\u00eb shumic\u00ebn e f\u00ebmij\u00ebve, simptomat zvog\u00eblohen me kalimin e koh\u00ebs ose zhduken spontanisht. Simptomat zakonisht nuk ndalen plot\u00ebsisht pas p\u00ebrdorimit t\u00eb ibuprofenit dhe paracetamolit, t\u00eb cil\u00ebt zakonisht ndihmojn\u00eb me infeksionet virale. Nj\u00eb doz\u00eb e vetme e kortikosteroideve, e dh\u00ebn\u00eb kur shfaqen simptomat, e shkurton koh\u00ebzgjatjen e nj\u00eb ataku. Prind\u00ebrit nuk guxojn\u00eb t&#8217;i japin k\u00ebto barna pa k\u00ebshill\u00ebn paraprake t\u00eb pediatrit dhe pa analizat dhe ekzaminimet e holl\u00ebsishme!<\/span><\/p>\n<p lang=\"mk-MK\"><span style=\"font-size: medium;\">Trajtimi p\u00ebrfshin terapi simptomatike t\u00eb simptomave t\u00eb manifestuara dhe p\u00ebrmir\u00ebsim t\u00eb cil\u00ebsis\u00eb s\u00eb jet\u00ebs. Terapia e suksesshme p\u00ebr menaxhimin e simptomave t\u00eb k\u00ebsaj sindrome p\u00ebrfshin: kortikosteroidet orale (Prednisone ose Prednisolone), tonsilektomin\u00eb, heqjen e adenoideve dhe Cimetidin\u00ebn. Ekipi i specialist\u00ebve q\u00eb ofrojn\u00eb kujdes p\u00ebr nj\u00eb pacient me sindrom\u00ebn PFAPA p\u00ebrfshin: pediat\u00ebr, otorinolaringolog, reumatolog.<\/span><\/p>\n\n<div style=\"font-size: 0px; height: 0px; line-height: 0px; margin: 0; padding: 0; clear: both;\"><\/div>","protected":false},"excerpt":{"rendered":"<p>Sindroma e etheve periodike, stomatit aftoz, faringjit dhe adenit cervikal\/PFAPA Syndrome ICD E 85.0 Prevalenca: e panjohur Ethet periodike, stomatiti [&hellip;]<\/p>\n","protected":false},"author":22,"featured_media":187824,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_mo_disable_npp":"no","inline_featured_image":false},"categories":[3087],"tags":[],"imageURL":"https:\/\/sdk.mk\/wp-content\/uploads\/2023\/02\/03-PFAPA-Syndrome-1-650x366.png","thumbURL":"https:\/\/sdk.mk\/wp-content\/uploads\/2023\/02\/03-PFAPA-Syndrome-1-250x141.png","categoryNames":["Maqedonia"],"feature_caption":"","subtitle":"","views":"749","source":"\u0421\u043a\u043e\u043f\u0458\u0435, (\u0421\u0410\u041a\u0410\u041c\u0414\u0410\u041a\u0410\u0416\u0410\u041c.\u041c\u041a)","yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v15.0 - 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