{"id":188185,"date":"2023-02-07T07:47:02","date_gmt":"2023-02-07T06:47:02","guid":{"rendered":"https:\/\/sdk.mk\/?p=188185"},"modified":"2023-02-07T07:47:02","modified_gmt":"2023-02-07T06:47:02","slug":"ju-njoftojme-me-semundjet-e-rralla-artrogripoza","status":"publish","type":"post","link":"https:\/\/sdk.mk\/index.php\/maqedonia\/ju-njoftojme-me-semundjet-e-rralla-artrogripoza\/","title":{"rendered":"JU NJOFTOJM\u00cb ME S\u00cbMUNDJET E RRALLA: ARTROGRIPOZA"},"content":{"rendered":"<div class=\"f52428582a4b906b2d2e2a7d733c7d27\" data-index=\"7\" style=\"float: none; margin:10px 0 10px 0; text-align:center;\">\n<!-- MSP Ads Asynchronous JS Tag - Generated with Revive Adserver v5.4.1 -->\r\n<ins data-revive-zoneid=\"167\" data-revive-id=\"060fdb01f6430ec164d3519234aa4967\"><\/ins>\r\n<script async src=\"\/\/panel.ads.com.mk\/www\/delivery\/asyncjs.php\"><\/script>\n<\/div>\n<p><a href=\"https:\/\/www.youtube.com\/watch?v=soZRAprwEQE&amp;list=PLPGcigDEy-qgR2zVetKogPsjWUrslN1gR&amp;index=7\" target=\"_blank\" rel=\"noopener noreferrer\"><em><strong>Artrogripoza<\/strong><\/em><\/a><br \/>\nICD 10 Q74.3<br \/>\nPrevalenca (prevalenca): 1\/3.000 t\u00eb porsalindur<\/p>\n<p>Artrogripoza \u00ebsht\u00eb nj\u00eb s\u00ebmundje e rrall\u00eb kongjenitale e karakterizuar nga zhvillimi i kontrakturave t\u00eb ky\u00e7eve q\u00eb prekin dy ose m\u00eb shum\u00eb rajone t\u00eb trupit. Kontraktura \u00ebsht\u00eb ngurt\u00ebsi e p\u00ebrhershme e nj\u00eb nyjeje n\u00eb nj\u00eb pozicion t\u00eb p\u00ebrkulur ose vertikal dhe ndikon n\u00eb funksionin e gjymtyr\u00ebve, nga funksioni i reduktuar deri te atrofia e plot\u00eb e muskujve. Kjo s\u00ebmundje nuk \u00ebsht\u00eb nj\u00eb s\u00ebmundje specifike, por nj\u00eb simptom\u00eb fizike q\u00eb shfaqet n\u00eb shumic\u00ebn e gjendjeve sh\u00ebndet\u00ebsore.<\/p>\n<p><em><strong>Shkaqet:<\/strong><\/em><\/p>\n<p>Supozohet se shkaku i artrogripoz\u00ebs jan\u00eb l\u00ebvizjet e reduktuara t\u00eb fetusit n\u00eb zhvillimin prenatal, e cila mund t\u00eb jet\u00eb pasoj\u00eb e shum\u00eb shkaqeve t\u00eb ndryshme, faktor\u00ebt e mjedisit (s\u00ebmundje t\u00eb n\u00ebn\u00ebs, hap\u00ebsira e kufizuar intrauterine), Mutacionet e gjeneve (autozomale dominante, autozomale recesive, t\u00eb lidhura me X), anomalit\u00eb kromozomale dhe sindrome t\u00eb ndryshme.<\/p>\n<p><em><strong>Simptomat:<\/strong><\/em><\/p>\n<p>Artrogripoza n\u00ebnkupton shfaqjen e kontrakturave t\u00eb shumta t\u00eb ky\u00e7eve, n\u00eb dy ose m\u00eb shum\u00eb vende t\u00eb trupit para lindjes. Kontreakturat ndodhin kur nyja \u00ebsht\u00eb e fiksuar n\u00eb nj\u00eb pozicion ku \u00ebsht\u00eb i p\u00ebrkulur dhe i drejtuar p\u00ebrgjithmon\u00eb, gj\u00eb q\u00eb kufizon funksionin dhe gam\u00ebn e l\u00ebvizjes s\u00eb ky\u00e7it.<\/p>\n<p>Tek disa pacient\u00eb jan\u00eb m\u00eb pak t\u00eb z\u00ebn\u00eb nyjet dhe diapazoni i l\u00ebvizjes \u00ebsht\u00eb pothuajse normal. Tek pacient\u00ebt tek t\u00eb cil\u00ebt s\u00ebmundja \u00ebsht\u00eb m\u00eb e zhvilluar, t\u00eb gjitha nyjet n\u00eb trup jan\u00eb t\u00eb prekura, duke p\u00ebrfshir\u00eb nofull\u00ebn dhe shpin\u00ebn. Muskujt rreth nyjeve t\u00eb prekura jan\u00eb t\u00eb atrofizuar ose t\u00eb pazhvilluar. Tek nyjet mundet te vij\u00eb edhe deri tek ngjitja e indeve te buta.<\/p>\n<p><em><strong>Parashikim:<\/strong><\/em><\/p>\n<p>Prognoza afatgjat\u00eb p\u00ebr njer\u00ebzit me artrogripoz\u00eb varet nga pesha e gjendjes, shkaku themelor dhe p\u00ebrgjigja ndaj terapis\u00eb.Shkalla e p\u00ebrfshirjes s\u00eb muskujve dhe ky\u00e7eve ndryshon nga personi n\u00eb person.<\/p>\n<p>N\u00eb p\u00ebrgjith\u00ebsi, prognoza p\u00ebr pacient\u00ebt me artrogripoz\u00eb \u00ebsht\u00eb e mir\u00eb. Me terapi fizike dhe trajtime t\u00eb tjera, \u00ebsht\u00eb e mundur t\u00eb arrihet nj\u00eb p\u00ebrmir\u00ebsim gradual i funksionit dhe l\u00ebvizshm\u00ebris\u00eb s\u00eb ky\u00e7eve. Shumica e pacient\u00ebve me artrogripoz\u00eb kan\u00eb inteligjenc\u00eb normale dhe b\u00ebjn\u00eb nj\u00eb jet\u00eb normale dhe t\u00eb pavarur si t\u00eb rritur, dhe 25% e pacient\u00ebve b\u00ebhen t\u00eb paaft\u00eb.<\/p>\n<p><em><strong>Mjekimi:<\/strong><\/em><\/p>\n<p>Trajtimi i artrogripoz\u00ebs ndryshon n\u00eb baz\u00eb t\u00eb shenjave dhe simptomave q\u00eb shfaqen te njer\u00ebz t\u00eb ndrysh\u00ebm. Q\u00ebllimi i trajtimit \u00ebsht\u00eb t\u00eb arrihet funksioni dhe aft\u00ebsia optimale p\u00ebr t\u00eb ngar\u00eb skuter\u00ebt elektrik\u00eb, si dhe komandimi I mjeteve me kompjuter.<br \/>\nInsistohet q\u00eb nj\u00ebri b\u00ebrryl t\u00eb jet\u00eb n\u00eb pozicion vertikal n\u00eb m\u00ebnyr\u00eb q\u00eb t\u00eb ruhet higjiena perianale dhe b\u00ebrryli tjet\u00ebr n\u00eb fleksion n\u00eb m\u00ebnyr\u00eb q\u00eb t\u00eb mund t\u00eb ushqehet n\u00eb m\u00ebnyr\u00eb t\u00eb pavarur. Trajtimi jokirurgjikal \u00ebsht\u00eb linja e par\u00eb e terapis\u00eb dhe p\u00ebrfshin manipulimin pasiv dhe vendosjen e gipsit.<\/p>\n<p>Trajtimet kirurgjikale konsistojn\u00eb n\u00eb heqjen e indeve t\u00eb buta, transferimin e tendinave dhe osteotomin\u00eb.<\/p>\n\n<div style=\"font-size: 0px; height: 0px; line-height: 0px; margin: 0; padding: 0; clear: both;\"><\/div>","protected":false},"excerpt":{"rendered":"<p>Artrogripoza ICD 10 Q74.3 Prevalenca (prevalenca): 1\/3.000 t\u00eb porsalindur Artrogripoza \u00ebsht\u00eb nj\u00eb s\u00ebmundje e rrall\u00eb kongjenitale e karakterizuar nga zhvillimi [&hellip;]<\/p>\n","protected":false},"author":24,"featured_media":188186,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_mo_disable_npp":"no","inline_featured_image":false},"categories":[3087],"tags":[],"imageURL":"https:\/\/sdk.mk\/wp-content\/uploads\/2023\/02\/07-Arthrogryposis-multiplex-congenita-1-650x366.png","thumbURL":"https:\/\/sdk.mk\/wp-content\/uploads\/2023\/02\/07-Arthrogryposis-multiplex-congenita-1-250x141.png","categoryNames":["Maqedonia"],"feature_caption":"","subtitle":"","views":"88","source":"\u0421\u043a\u043e\u043f\u0458\u0435, (\u0421\u0410\u041a\u0410\u041c\u0414\u0410\u041a\u0410\u0416\u0410\u041c.\u041c\u041a)","yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v15.0 - 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