{"id":189119,"date":"2023-02-20T08:03:22","date_gmt":"2023-02-20T07:03:22","guid":{"rendered":"https:\/\/sdk.mk\/?p=189119"},"modified":"2023-02-20T08:03:22","modified_gmt":"2023-02-20T07:03:22","slug":"ju-njoftojme-me-semundjet-e-rralla-syringomyelia","status":"publish","type":"post","link":"https:\/\/sdk.mk\/index.php\/maqedonia\/ju-njoftojme-me-semundjet-e-rralla-syringomyelia\/","title":{"rendered":"JU NJOFTOJM\u00cb ME S\u00cbMUNDJET E RRALLA: SYRINGOMYELIA"},"content":{"rendered":"<div class=\"f52428582a4b906b2d2e2a7d733c7d27\" data-index=\"7\" style=\"float: none; margin:10px 0 10px 0; text-align:center;\">\n<!-- MSP Ads Asynchronous JS Tag - Generated with Revive Adserver v5.4.1 -->\r\n<ins data-revive-zoneid=\"167\" data-revive-id=\"060fdb01f6430ec164d3519234aa4967\"><\/ins>\r\n<script async src=\"\/\/panel.ads.com.mk\/www\/delivery\/asyncjs.php\"><\/script>\n<\/div>\n<p lang=\"mk-MK\"><em><strong><span style=\"font-size: medium;\">Syringomyelia<\/span><\/strong><\/em><\/p>\n<p lang=\"mk-MK\"><span style=\"font-size: medium;\">ICD10: G95.0<\/span><\/p>\n<p lang=\"mk-MK\"><span style=\"font-size: medium;\">Prevalenca : 1-9\/ 100.000<\/span><\/p>\n<p lang=\"mk-MK\"><span style=\"font-size: medium;\">Syringomyelia \u00ebsht\u00eb nj\u00eb gjendje e karakterizuar nga nj\u00eb ose cist\u00eb e mbushur me l\u00ebng i cili njihet si nj\u00eb syrinks q\u00eb formohet n\u00eb palc\u00ebn kurrizore. Syringomyelia \u00ebsht\u00eb nj\u00eb gjendje kronike dhe syrinksi mund t\u00eb zmadhohet me kalimin e koh\u00ebs dhe t\u00eb kompresoj\u00eb ose shkat\u00ebrroj\u00eb indin nervor p\u00ebrreth. Nj\u00eb gam\u00eb e gjer\u00eb simptomash mund t\u00eb shoq\u00ebrohen potencialisht me siringomyelin\u00eb n\u00eb var\u00ebsi t\u00eb madh\u00ebsis\u00eb dhe vendndodhjes s\u00eb sakt\u00eb t\u00eb syrinksit. Shenjat\/simptomat e zakonshme p\u00ebrfshijn\u00eb dhimbje n\u00eb qaf\u00eb dhe dhimbje shpatullash, dob\u00ebsi muskulore, dhimbje dhe ngurrt\u00ebsi n\u00eb k\u00ebmb\u00eb, ulje e ndjesis\u00eb s\u00eb ftoht\u00ebsis\u00eb dhe nxet\u00ebsis\u00eb, shtremb\u00ebrime t\u00eb kurrizit- skolioz\u00eb), kontraktime muskulore dhe l\u00ebvizje t\u00eb pakoordinuara (ataksi). Shumica e rasteve t\u00eb siringomielis\u00eb shoq\u00ebrohen me nj\u00eb anomali komplekse t\u00eb trurit t\u00eb njohur si keqformim Chiari. Shkaqe t\u00eb tjera t\u00eb njohura t\u00eb siringomielis\u00eb p\u00ebrfshijn\u00eb encefalitin, meningjitin (arachnoiditis), disa tumore t\u00eb palc\u00ebs kurrizore dhe traumat. N\u00eb disa pacient\u00eb, shkaku themelor (idiopatik) nuk mund t\u00eb identifikohet.<\/span><\/p>\n<p lang=\"mk-MK\"><span style=\"font-size: medium;\"><b>P\u00ebrshkrimi klinik:<\/b><\/span><\/p>\n<p lang=\"mk-MK\"><span style=\"font-size: medium;\">Edhe pse siringomyelia mund t\u00eb shkaktoj\u00eb nd\u00ebrprerje t\u00eb lidhjeve nervore n\u00eb palc\u00ebn kurrizore dhe d\u00ebmtime neurologjike, 50% e pacient\u00ebve (kur merren parasysh t\u00eb gjitha llojet e syrinksit) nuk p\u00ebrjetojn\u00eb ndyrhsime t\u00eb atilla ose kan\u00eb vet\u00ebm nj\u00eb paaft\u00ebsi t\u00eb leht\u00eb. N\u00eb pacient\u00ebt simptomatik\u00eb, fillimi zakonisht tregohet nga s\u00ebmundje dhe shqet\u00ebsime shqisore, t\u00eb cilat variojn\u00eb nga mungesa e plot\u00eb e ndjesis\u00eb,si shpimi me gjilp\u00ebra ose ndryshimi i temperatures deri tek ndjeshm\u00ebria e teprurar nga stimulimet e ndryshme.. Megjith\u00ebse nuk ka indikacione t\u00eb qarta klinike n\u00eb ekzaminimin neurologjik, disocimi I ndjesave (humbja e aft\u00ebsis\u00eb p\u00ebr t\u00eb dalluar nxeht\u00ebsin\u00eb nga t\u00eb ftohtit n\u00eb gjymtyr\u00ebt e sip\u00ebrme), si dhe reduktimi i reflekseve t\u00eb gjymtyr\u00ebve t\u00eb sip\u00ebrme, jan\u00eb ndryshime fillestare mjaft specifike kur jan\u00eb t\u00eb pranishme. Simptomat motorike zakonisht variojn\u00eb nga shkall\u00eb t\u00eb ndryshme dob\u00ebsie deri n\u00eb spasticitet dhe humbje t\u00eb autonomis\u00eb. Mund t\u00eb jen\u00eb t\u00eb pranishme edhe ndryshime n\u00eb fshik\u00ebz\u00ebn urinare dhe funksionin seksual. Individ\u00ebt e prekur gjithashtu mund t\u00eb zhvillojn\u00eb dhimbje dhe ngurt\u00ebsi (spasticitet) n\u00eb k\u00ebmb\u00eb dhe l\u00ebvizje t\u00eb pakoordinuara (ataksi), t\u00eb cilat p\u00ebrfundimisht do t\u00eb ndikojn\u00eb n\u00eb aft\u00ebsin\u00eb p\u00ebr t\u00eb ecur. N\u00eb raste t\u00eb r\u00ebnda, mund t\u00eb ndodh\u00eb paraliza e krah\u00ebve ose k\u00ebmb\u00ebve. Disa individ\u00eb t\u00eb prekur mund t\u00eb zhvillojn\u00eb kontraktime t\u00eb muskujve t\u00eb tilla si kontraktime t\u00eb vogla, t\u00eb pavullnetshme t\u00eb muskujve ose &#8220;dridhje&#8221; (fascikulacione). Anomalit\u00eb e skeletit mund t\u00eb zhvillohen, duke p\u00ebrfshir\u00eb nj\u00eb lakim jonormal t\u00eb shtyll\u00ebs kurrizore (skolioz\u00eb). N\u00eb disa f\u00ebmij\u00eb, skolioza mund t\u00eb jet\u00eb simptoma e vetme. Disa individ\u00eb mund t\u00eb zhvillojn\u00eb nyje Charcot, n\u00eb t\u00eb cilat ndodh degjenerimi kronik progresiv i ky\u00e7it p\u00ebr shkak t\u00eb d\u00ebmtimit t\u00eb nervave q\u00eb furnizojn\u00eb nyjen. Tek k\u00ebto nyje fillimisht shihen \u00ebnjtje dhe skuqje t\u00eb zonave t\u00eb prekura. Pa trajtim, mund t\u00eb ndodh\u00eb deformim i nyjeve t\u00eb prekura. Disa individ\u00eb t\u00eb prekur zhvillojn\u00eb simptoma q\u00eb lidhen me d\u00ebmtimin e sistemit nervor autonom, i cili \u00ebsht\u00eb pjesa e sistemit nervor q\u00eb kontrollon funksionet e pavullnetshme. Simptoma t\u00eb tilla p\u00ebrfshijn\u00eb humbjen e kontrollit t\u00eb zorr\u00ebve dhe fshik\u00ebz\u00ebs, djersitje t\u00eb tep\u00ebrt (hiperhidroz\u00eb) dhe luhatje t\u00eb niveleve t\u00eb presionit t\u00eb gjakut. Mund t\u00eb ndodh\u00eb gjithashtu sindroma e Hornerit, nj\u00eb gjendje e pazakont\u00eb q\u00eb zhvillohet p\u00ebr shkak t\u00eb d\u00ebmtimit t\u00eb nj\u00ebrit prej nervave q\u00eb furnizon syt\u00eb dhe fytyr\u00ebn. Sindroma e Hornerit zakonisht prek nj\u00ebr\u00ebn an\u00eb t\u00eb fytyr\u00ebs dhe karakterizohet nga r\u00ebnia e qepallave, ngushtimi i hapjes midis qepallave, zvog\u00eblimi i madh\u00ebsis\u00eb s\u00eb beb\u00ebz\u00ebs dhe pak\u00ebsimi i djersitjes n\u00eb an\u00ebn e prekur t\u00eb fytyr\u00ebs.<\/span><\/p>\n<p lang=\"mk-MK\"><span style=\"font-size: medium;\">Pacient\u00ebt me siringomieli, t\u00eb shoq\u00ebruar me nj\u00eb keqformim Chiari, mund t\u00eb ken\u00eb gjithashtu nj\u00eb gjendje t\u00eb quajtur hidrocefalus, n\u00eb t\u00eb cil\u00ebn ka nj\u00eb akumulim jonormal t\u00eb l\u00ebngut cerebrospinal n\u00eb tru. N\u00eb f\u00ebmij\u00ebri, hidrocefalusi mund t\u00eb shkaktoj\u00eb nj\u00eb s\u00ebr\u00eb simptomash, duke p\u00ebrfshir\u00eb zmadhimin e kok\u00ebs, t\u00eb vjella, dhimbje koke, p\u00ebrgjumje, nervoziz\u00ebm, kriza dhe nistagmus.<\/span><\/p>\n<p lang=\"mk-MK\"><span style=\"font-size: medium;\"><b>Metodat diagnostikuese:<\/b><\/span><\/p>\n<p lang=\"mk-MK\"><span style=\"font-size: medium;\">P\u00ebr diagnoz\u00ebn k\u00ebrkohet nj\u00eb ekzaminim neurologjik dhe MRI. MRI \u00ebsht\u00eb standardi i art\u00eb dhe zbulon nj\u00eb zgav\u00ebr t\u00eb mbushur me l\u00ebng me shkall\u00eb t\u00eb ndryshueshme shtrirjeje vertikale dhe horizontale brenda palc\u00ebs kurrizore, duke filluar nga p\u00ebrfshirja n\u00eb nj\u00eb nivel deri n\u00eb shtrirjen e t\u00eb gjith\u00eb palc\u00ebs kurrizore. Karakteristikat e sinjalit t\u00eb MRI jan\u00eb zakonisht mjaft t\u00eb ngjashme me ato t\u00eb CSF.<\/span><\/p>\n<p lang=\"mk-MK\"><span style=\"font-size: medium;\"><b>Menaxhimi dhe trajtimi:<\/b><\/span><\/p>\n<p lang=\"mk-MK\"><span style=\"font-size: medium;\">Menaxhimi konsiston n\u00eb ndjekjen afatgjat\u00eb dhe kirurgjin\u00eb n\u00eb rastet e p\u00ebrkeq\u00ebsimit neurologjik progresiv. Lloji i operacionit p\u00ebrcaktohet nga lloji dhe shkaku themelor i syrinksit. N\u00eb PS, zhvendosja e drejtp\u00ebrdrejt\u00eb e syrinksit n\u00eb hap\u00ebsir\u00ebn subaraknoidale t\u00eb shtyll\u00ebs kurrizore, zgavr\u00ebn pleurale ose peritoneale \u00ebsht\u00eb e vetmja mund\u00ebsi trajtimi. N\u00eb SS, trajtimi sillet rreth korrigjimit t\u00eb shkakut themelor dhe varet shum\u00eb nga preferencat dhe p\u00ebrvoja e kirurgut.<\/span><\/p>\n<p lang=\"mk-MK\"><span style=\"font-size: medium;\"><b>Terapit\u00eb standarde:<\/b><\/span><\/p>\n<p lang=\"mk-MK\"><span style=\"font-size: medium;\">Trajtimi i siringomyelis\u00eb drejtohet n\u00eb simptomat specifike q\u00eb jan\u00eb evidente tek \u00e7do individ. Trajtimi mund t\u00eb k\u00ebrkoj\u00eb p\u00ebrpjekjet e koordinuara t\u00eb nj\u00eb ekipi specialist\u00ebsh<\/span><\/p>\n<p lang=\"mk-MK\"><span style=\"font-size: medium;\">Procedurat dhe nd\u00ebrhyrjet specifike terapeutike mund t\u00eb ndryshojn\u00eb, n\u00eb var\u00ebsi t\u00eb nj\u00eb s\u00ebr\u00eb faktor\u00ebsh, t\u00eb till\u00eb si p\u00ebrparimi i s\u00ebmundjes, prania ose mungesa e simptomave t\u00eb caktuara, shkaku themelor, ndikimi i simptomave n\u00eb cil\u00ebsin\u00eb e jet\u00ebs, mosha e individit dhe sh\u00ebndeti i p\u00ebrgjithsh\u00ebm. , dhe\/ose elemente t\u00eb tjera. Vendimet n\u00eb lidhje me p\u00ebrdorimin e regjimeve t\u00eb ve\u00e7anta t\u00eb barnave dhe\/ose trajtime t\u00eb tjera duhet t\u00eb merren nga mjek\u00ebt dhe an\u00ebtar\u00ebt e tjer\u00eb t\u00eb ekipit t\u00eb kujdesit sh\u00ebndet\u00ebsor n\u00eb konsultim t\u00eb kujdessh\u00ebm me pacientin bazuar n\u00eb specifikat e rastit t\u00eb tij ose t\u00eb saj, nj\u00eb diskutim t\u00eb plot\u00eb t\u00eb p\u00ebrfitimeve dhe rreziqeve t\u00eb mundshme. , duke p\u00ebrfshir\u00eb efektet e mundshme an\u00ebsore dhe efektet afatgjata, preferencat e pacientit dhe faktor\u00eb t\u00eb tjer\u00eb t\u00eb r\u00ebnd\u00ebsish\u00ebm.<\/span><\/p>\n<p lang=\"mk-MK\"><span style=\"font-size: medium;\">Disa njer\u00ebz me siringomieli q\u00eb nuk kan\u00eb simptoma mund t\u00eb mos k\u00ebrkojn\u00eb trajtim, por duhet t\u00eb monitorohen rregullisht p\u00ebr t\u00eb par\u00eb n\u00ebse \u00e7\u2019rregullimi po p\u00ebrparon. Opsionet e p\u00ebrgjithshme terapeutike p\u00ebrfshijn\u00eb ila\u00e7e kund\u00ebr dhimbjeve (analgjezik\u00eb), terapi fizike dhe aktivitete reduktuese, ve\u00e7an\u00ebrisht ato q\u00eb k\u00ebrkojn\u00eb sforcim, si\u00e7 \u00ebsht\u00eb ngritja e peshave. Q\u00ebllimi i trajtimit p\u00ebr siringomielin\u00eb \u00ebsht\u00eb t\u00eb rivendos\u00eb rrjedh\u00ebn e duhur t\u00eb l\u00ebngut cerebrospinal dhe t\u00eb heq\u00eb presionin q\u00eb syrinksi ushtron n\u00eb palc\u00ebn kurrizore. Trajtimi fillestar zakonisht synon shkakun themelor t\u00eb siringomielis\u00eb. Kirurgjia rekomandohet p\u00ebr njer\u00ebzit me p\u00ebrkeq\u00ebsim neurologjik dhe\/ose dhimbje t\u00eb patrajtueshme. Operacioni ka p\u00ebr q\u00ebllim zgjerimin e zon\u00ebs rreth palc\u00ebs kurrizore n\u00eb vendin e traum\u00ebs ose l\u00ebndimit dhe zvog\u00eblimin e v\u00ebllimit t\u00eb l\u00ebngjeve. Kirurgjia p\u00ebr siringomieli shpesh mund t\u00eb \u00e7oj\u00eb n\u00eb p\u00ebrmir\u00ebsimin e simptomave dhe stabilizimin e \u00e7rregullimit n\u00eb shum\u00eb individ\u00eb. Megjithat\u00eb, siringomyelia mund t\u00eb p\u00ebrs\u00ebritet pas trajtimit t\u00eb suksessh\u00ebm, duke k\u00ebrkuar operacione t\u00eb shumta.<\/span><\/p>\n\n<div style=\"font-size: 0px; height: 0px; line-height: 0px; margin: 0; padding: 0; clear: both;\"><\/div>","protected":false},"excerpt":{"rendered":"<p>Syringomyelia ICD10: G95.0 Prevalenca : 1-9\/ 100.000 Syringomyelia \u00ebsht\u00eb nj\u00eb gjendje e karakterizuar nga nj\u00eb ose cist\u00eb e mbushur me [&hellip;]<\/p>\n","protected":false},"author":22,"featured_media":189120,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_mo_disable_npp":"no","inline_featured_image":false},"categories":[3087],"tags":[],"imageURL":"https:\/\/sdk.mk\/wp-content\/uploads\/2023\/02\/20-Syringomyelia-1-650x366.png","thumbURL":"https:\/\/sdk.mk\/wp-content\/uploads\/2023\/02\/20-Syringomyelia-1-250x141.png","categoryNames":["Maqedonia"],"feature_caption":"","subtitle":"","views":"558","source":"\u0421\u043a\u043e\u043f\u0458\u0435, (\u0421\u0410\u041a\u0410\u041c\u0414\u0410\u041a\u0410\u0416\u0410\u041c.\u041c\u041a)","yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v15.0 - 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