{"id":189804,"date":"2023-02-28T07:59:13","date_gmt":"2023-02-28T06:59:13","guid":{"rendered":"https:\/\/sdk.mk\/?p=189804"},"modified":"2023-02-28T07:59:13","modified_gmt":"2023-02-28T06:59:13","slug":"ju-njoftojme-me-semundjet-e-rralla-nevusi-gjigant-kongjenital","status":"publish","type":"post","link":"https:\/\/sdk.mk\/index.php\/maqedonia\/ju-njoftojme-me-semundjet-e-rralla-nevusi-gjigant-kongjenital\/","title":{"rendered":"JU NJOFTOJM\u00cb ME S\u00cbMUNDJET E RRALLA: NEVUSI GJIGANT KONGJENITAL"},"content":{"rendered":"<div class=\"f52428582a4b906b2d2e2a7d733c7d27\" data-index=\"7\" style=\"float: none; margin:10px 0 10px 0; text-align:center;\">\n<!-- MSP Ads Asynchronous JS Tag - Generated with Revive Adserver v5.4.1 -->\r\n<ins data-revive-zoneid=\"167\" data-revive-id=\"060fdb01f6430ec164d3519234aa4967\"><\/ins>\r\n<script async src=\"\/\/panel.ads.com.mk\/www\/delivery\/asyncjs.php\"><\/script>\n<\/div>\n<p><a href=\"https:\/\/www.youtube.com\/watch?v=2YMf1Hcm26g&amp;list=PLPGcigDEy-qgR2zVetKogPsjWUrslN1gR&amp;index=28\" target=\"_blank\" rel=\"noopener noreferrer\"><em><strong>Nevusi gjigant kongjenital<\/strong><\/em><\/a><\/p>\n<p><b>ICD10:\u00a0 D22<\/b><\/p>\n<p><b>Prevalenca: m\u00eb pak se 1-20.000 t\u00eb porsalindur<\/b><\/p>\n<p><span style=\"font-weight: 400;\">NevusI gjigant kongjenital \u00ebsht\u00eb nj\u00eb pjes\u00eb e l\u00ebkur\u00ebs me ngjyr\u00eb t\u00eb err\u00ebt, shpesh me qime, e pranishme n\u00eb lindje (ndryshim kongjenital) dhe rritet n\u00eb p\u00ebrpjes\u00ebtim me rritjen e f\u00ebmij\u00ebs. Nevusi kongjenital i pigmentuar konsiderohet gjigant n\u00ebse \u00ebsht\u00eb m\u00eb i madh se 20 cm n\u00eb diamet\u00ebr deri n\u00eb pubertet. Nevuse gjigante kongjenitale mund t\u00eb shfaqen te njer\u00ebzit e \u00e7do race apo etnie dhe n\u00eb \u00e7do zon\u00eb t\u00eb trupit. Ato jan\u00eb rezultat i ndryshimeve gjenetike t\u00eb lokalizuara n\u00eb fetus q\u00eb \u00e7ojn\u00eb n\u00eb nj\u00eb rritje t\u00eb tep\u00ebrt t\u00eb melanociteve, qelizat n\u00eb l\u00ebkur\u00eb q\u00eb jan\u00eb p\u00ebrgjegj\u00ebse p\u00ebr ngjyr\u00ebn e l\u00ebkur\u00ebs.<\/span><\/p>\n<p><b>Patogjeneza:<\/b><\/p>\n<p><span style=\"font-weight: 400;\">JVN ndodh midis jav\u00ebs s\u00eb 5-t\u00eb dhe 24-t\u00eb t\u00eb shtatz\u00ebnis\u00eb. Besohet se gjat\u00eb embriogjenez\u00ebs ndodh nj\u00eb gabim morfologjik n\u00eb neuroektoderm\u00eb q\u00eb \u00e7on n\u00eb rritjen e parregulluar t\u00eb melanoblasteve, qelizat pararend\u00ebse t\u00eb melanociteve. Megjithat\u00eb, histogjeneza e nevuseve melanocitare \u00ebsht\u00eb ende nj\u00eb \u00e7\u00ebshtje polemike.<\/span><\/p>\n<p><b>Simptomat:<\/b><\/p>\n<p><span style=\"font-weight: 400;\">Njer\u00ebzit me nevuse kongjenitale gjigante mund t\u00eb mos ken\u00eb simptoma t\u00eb tjera ose mund t\u00eb ken\u00eb pak simptoma t\u00eb tilla si l\u00ebkur\u00eb e that\u00eb, e trash\u00eb ose kruarje t\u00eb tep\u00ebrt. N\u00eb rreth 5% deri n\u00eb 10% t\u00eb rasteve, nj\u00eb nevus gjigant kongjenital shoq\u00ebrohet me melanocitoz\u00eb neurokutane (nj\u00eb tepric\u00eb e qelizave t\u00eb pigmentit n\u00eb tru ose n\u00eb palc\u00ebn kurrizore) dhe karakterizohet me simptoma neurologjike. Ata gjithashtu kan\u00eb nj\u00eb rrezik t\u00eb shtuar t\u00eb zhvillimit t\u00eb melanom\u00ebs malinje, nj\u00eb lloj kanceri i l\u00ebkur\u00ebs, ve\u00e7an\u00ebrisht n\u00ebse nevusi \u00ebsht\u00eb i lokalizuar n\u00eb shtyll\u00ebn kurrizore ose kur ka lezione t\u00eb shumta shoq\u00ebruese.<\/span><\/p>\n<p><b>Diagnoza:<\/b><\/p>\n<p><span style=\"font-weight: 400;\">Diagnoza \u00ebsht\u00eb kryesisht klinike. Nga pik\u00ebpamja histologjike, megjithat\u00eb, JVN n\u00eb p\u00ebrgjith\u00ebsi dallohet nga nj\u00eb nevus i fituar kryesisht nga madh\u00ebsia e tij, p\u00ebrhapja e qelizave nevus n\u00eb shtresat m\u00eb t\u00eb thella t\u00eb l\u00ebkur\u00ebs (p\u00ebrfshir\u00eb indet n\u00ebnl\u00ebkurore) dhe arkitektur\u00ebn dhe morfologjin\u00eb e saj t\u00eb ndryshme.<\/span><\/p>\n<p><b>Evolucioni dhe prognoza:<\/b><\/p>\n<p><span style=\"font-weight: 400;\">Me kalimin e koh\u00ebs, JVN mund t&#8217;i n\u00ebnshtrohet nj\u00eb procesi err\u00ebsimi ose ndri\u00e7imi, t\u00eb zhvilloj\u00eb pigmentim m\u00eb heterogjen ose homogjen, t\u00eb shfaqet me nj\u00eb rritje t\u00eb rritjes s\u00eb flok\u00ebve, t\u00eb fitoj\u00eb nj\u00eb sip\u00ebrfaqe m\u00eb t\u00eb parregullt ose, m\u00eb rrall\u00eb, t\u00eb regresohet spontanisht. Disa autor\u00eb kan\u00eb v\u00ebrejtur nj\u00eb tendenc\u00eb fillestare q\u00eb lezionet t\u00eb err\u00ebsohen gjat\u00eb adoleshenc\u00ebs, t\u00eb ndjekur nga ndri\u00e7imi i konsideruesh\u00ebm, i shoq\u00ebruar me nj\u00eb rritje t\u00eb vrazhd\u00ebsis\u00eb s\u00eb sip\u00ebrfaqes dhe shfaqjen e hipertrikoz\u00ebs. N\u00eb p\u00ebrgjith\u00ebsi, lezionet kan\u00eb tendenc\u00eb t\u00eb trashen me kalimin e koh\u00ebs. Shfaqja e nyjeve n\u00eb nevus zakonisht korrespondon me p\u00ebrhapjen e elementeve t\u00eb indit neuroid. Nj\u00eb shqet\u00ebsim i madh p\u00ebr k\u00ebta pacient\u00eb \u00ebsht\u00eb mund\u00ebsia e zhvillimit t\u00eb melanom\u00ebs. Kur melanoma shfaqet n\u00eb JVN, prognoza \u00ebsht\u00eb ve\u00e7an\u00ebrisht e keqe.<\/span><\/p>\n<p>&nbsp;<\/p>\n<p><b>Mjekimi:<\/b><\/p>\n<p>&nbsp;<\/p>\n<p><span style=\"font-weight: 400;\">Qasja ndaj k\u00ebsaj s\u00ebmundjeje \u00ebsht\u00eb nj\u00eb sfid\u00eb dhe duhet t\u00eb individualizohet duke marr\u00eb parasysh: mosh\u00ebn e pacientit, madh\u00ebsin\u00eb dhe vendndodhjen e lezionit, rrezikun e progresionit n\u00eb melanoma, mund\u00ebsin\u00eb e NCM t\u00eb nj\u00ebkohshme, pranin\u00eb e ndryshimeve q\u00eb tregojn\u00eb malinjitet t\u00eb nevusit,\u00a0 d\u00ebmtime t\u00eb mundshme funksionale q\u00eb vijn\u00eb nga procedurat invazive dhe ndikimi psikologjik i lidhur me CMN ose plag\u00ebt kirurgjikale, shpesh t\u00eb tmerrshme. K\u00ebshtu, trajtimi i pacient\u00ebve me JVN mund t\u00eb p\u00ebrfshij\u00eb procedura kirurgjikale ose jokirurgjikale, nd\u00ebrhyrje psikologjike dhe klinike, me v\u00ebmendjen m\u00eb t\u00eb madhe ndaj ndryshimeve n\u00eb ngjyr\u00ebn, struktur\u00ebn ose sip\u00ebrfaqen e lezionit. Vendimi n\u00ebse nj\u00eb pacient duhet t&#8217;i n\u00ebnshtrohet apo jo trajtimit kirurgjik p\u00ebrfshin si v\u00ebshtir\u00ebsit\u00eb teknike n\u00eb kryerjen e procedurave t\u00eb tilla (ve\u00e7an\u00ebrisht kur merren parasysh motivimet kozmetike) ashtu edhe pasigurin\u00eb n\u00eb lidhje me efikasitetin e tij si nj\u00eb profilaks\u00eb e melanom\u00ebs.<\/span><\/p>\n\n<div style=\"font-size: 0px; height: 0px; line-height: 0px; margin: 0; padding: 0; clear: both;\"><\/div>","protected":false},"excerpt":{"rendered":"<p>Nevusi gjigant kongjenital ICD10:\u00a0 D22 Prevalenca: m\u00eb pak se 1-20.000 t\u00eb porsalindur NevusI gjigant kongjenital \u00ebsht\u00eb nj\u00eb pjes\u00eb e l\u00ebkur\u00ebs [&hellip;]<\/p>\n","protected":false},"author":24,"featured_media":189805,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_mo_disable_npp":"no","inline_featured_image":false},"categories":[3087],"tags":[],"imageURL":"https:\/\/sdk.mk\/wp-content\/uploads\/2023\/02\/28-Giant-congenital-nevus-1-650x366.png","thumbURL":"https:\/\/sdk.mk\/wp-content\/uploads\/2023\/02\/28-Giant-congenital-nevus-1-250x141.png","categoryNames":["Maqedonia"],"feature_caption":"","subtitle":"","views":"167","source":"\u0421\u043a\u043e\u043f\u0458\u0435, (\u0421\u0410\u041a\u0410\u041c\u0414\u0410\u041a\u0410\u0416\u0410\u041c.\u041c\u041a)","yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v15.0 - 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